| Rank (Similarity) |
PMID (PMCID) |
|
|---|---|---|
| 1 (48.0%) |
24772740 |
Leukemoid reaction, a rare manifestation of autoimmune hemolytic anemia in a case of small duct primary sclerosing cholangitis. Salagre KD, Sahay RN, Patil A, Pati A, Joshi A, Shukla A. J Assoc Physicians India. 2013;61(10):760-2. |
| Jaundice Hemolytic anemia | ||
| Adrenal Cortex Hormones Cholangitis, Sclerosing Differential Diagnosis Females Homo sapiens Leukemoid Reaction Middle Aged | ||
| 1 (48.0%) |
15492611 |
Rapid progression of autoimmune hepatitis in the background of primary sclerosing cholangitis. Hong-Curtis J, Yeh MM, Jain D, Lee JH. J Clin Gastroenterol. 2004;38(10):906-9. |
| Jaundice Hemolytic anemia | ||
| Adult Autoimmune Chronic Hepatitis Biopsy Blood Chemical Analysis Cholangitis, Sclerosing Disease Progression Endoscopic Retrograde Cholangiopancreatography Females Glucocorticoids Homo sapiens Liver Liver Function Tests Ulcerative Colitis | ||
| 1 (48.0%) |
7851854 |
Successful treatment of primary sclerosing cholangitis with cyclosporine and corticosteroid. Kyokane K, Ichihara T, Horisawa M, Suzuki N, Ichihara S, Suga S, Nakao A, Morise K. Hepatogastroenterology. 1994;41(5):449-52. |
| Jaundice Anemia | ||
| Cholangitis, Sclerosing Combination Drug Therapy Homo sapiens Male Pancreatic Diseases Remission Induction | ||
| 4 (44.2%) |
10365542 |
Primary sclerosing cholangitis in a child. Lin WT, Lin SJ, Ni YH, Chen HL, Wang HP, Chu JS, Chang MH. J Formos Med Assoc. 1999;98(3):209-13. |
| Eosinophilia Fever Hepatomegaly | ||
| Age of Onset Child, Preschool Cholagogues and Choleretics Cholangitis, Sclerosing Endoscopic Retrograde Cholangiopancreatography Eosinophilia Females Homo sapiens Liver Taiwan | ||
| 5 (43.7%) |
18589191 |
Tumor necrosis factor-alpha inhibitor-induced lupus-like syndrome presenting as fever of unknown origin in a liver transplant recipient: case report and concise review of the literature. Page AV, Liles WC. Transplant Proc. 2008;40(5):1768-70. |
| Anemia Fever Ulcerative colitis | ||
| TNF | ||
| Adult Anti-Inflammatory Agents Antibodies, Monoclonal, Humanized Fever of Unknown Origin Homo sapiens Lupus Erythematosus, Systemic Male Monoclonal Antibodies Postoperative Complications Tumor Necrosis Factor-alpha | ||
| 5 (43.7%) |
1568030 |
A case of primary intrahepatic sclerosing cholangitis (PISC) complicated with atypical biliary epithelial proliferation. Aizawa K, Kawaguchi S, Doi M, Mizuno W, Uragami K, Oka T, Miyamoto H, Itoh H, Nishioka S. Intern Med. 1992;31(1):114-21. |
| Anemia Duodenal ulcer Elevated alkaline phosphatase | ||
| Bile Duct Neoplasms Cholangitis, Sclerosing Differential Diagnosis Endoscopic Retrograde Cholangiopancreatography Epithelium Females Homo sapiens | ||
| 7 (43.3%) |
8887045 |
Primary sclerosing cholangitis associated with increased peripheral eosinophils and serum IgE. Shimomura I, Takase Y, Matsumoto S, Kuyama J, Nakajima T, Maeda H, Sugase T, Hata A, Hanada M, Okuno M. J Gastroenterol. 1996;31(5):737-41. |
| Jaundice Eosinophilia Fever | ||
| IGHE | ||
| Adult Cholangitis, Sclerosing Differential Diagnosis Endoscopic Retrograde Cholangiopancreatography Eosinophilia Glucocorticoids Homo sapiens Immunoglobulin E Male | ||
| 7 (43.3%) |
8213721 |
Eosinophilic sclerosing cholangitis associated with hypereosinophilic syndrome. Grauer L, Padilla VM 3rd, Bouza L, Barkin JS. Am J Gastroenterol. 1993;88(10):1764-9. |
| Jaundice Eosinophilia Fever | ||
| Adult Cholangitis, Sclerosing Homo sapiens Male | ||
| 9 (42.4%) |
8525344 |
[Pruritus--also a challenge in internal medicine]. Brunner W. Schweiz Med Wochenschr. 1995;125(46):2244-50. |
| Diabetes mellitus Cholestasis Leukemia | ||
| Adult Cholangitis, Sclerosing Differential Diagnosis Females Hematological Disease Hodgkin Disease Homo sapiens Male Metabolic Diseases Middle Aged Polycythemia Vera Pruritus Uremia | ||
| 10 (40.4%) |
15624373 |
A child with primary sclerosing cholangitis successfully treated by liver transplantation. Chen CH, Ho MC, Lee PH, Chang MH, Jeng YM, Ni YH. Acta Paediatr Taiwan. 2004;45(4):239-41. |
| Jaundice Splenomegaly Fever | ||
| Abdominal Pain Child Cholangitis, Sclerosing Endoscopic Retrograde Cholangiopancreatography Females Fever Homo sapiens |
Total: 55
| HPO ID | Term | Frequency |
|---|---|---|
| HP:0001396 | Cholestasis | Very frequent (99-80%) |
| HP:0002960 | Autoimmunity | Very frequent (99-80%) |
| HP:0012440 | Abnormal biliary tract morphology | Very frequent (99-80%) |
| HP:0001394 | Cirrhosis | Frequent (79-30%) |
| HP:0001395 | Hepatic fibrosis | Frequent (79-30%) |
| HP:0001409 | Portal hypertension | Frequent (79-30%) |
| HP:0001433 | Hepatosplenomegaly | Frequent (79-30%) |
| HP:0001541 | Ascites | Frequent (79-30%) |
| HP:0001744 | Splenomegaly | Frequent (79-30%) |
| HP:0001824 | Weight loss | Frequent (79-30%) |
| HP:0001945 | Fever | Frequent (79-30%) |
| HP:0002240 | Hepatomegaly | Frequent (79-30%) |
| HP:0002910 | Elevated hepatic transaminase | Frequent (79-30%) |
| HP:0010638 | Elevated alkaline phosphatase of hepatic origin | Frequent (79-30%) |
| HP:0012522 | Spider hemangioma | Frequent (79-30%) |
| HP:0012700 | Abnormal large intestine physiology | Frequent (79-30%) |
| HP:0030168 | Dilated superficial abdominal veins | Frequent (79-30%) |
| HP:0100279 | Ulcerative colitis | Frequent (79-30%) |
| HP:0100869 | Palmar telangiectasia | Frequent (79-30%) |
| HP:0000083 | Renal insufficiency | Occasional (29-5%) |
| HP:0000716 | Depressivity | Occasional (29-5%) |
| HP:0000938 | Osteopenia | Occasional (29-5%) |
| HP:0000939 | Osteoporosis | Occasional (29-5%) |
| HP:0000952 | Jaundice | Occasional (29-5%) |
| HP:0000989 | Pruritus | Occasional (29-5%) |
| HP:0001081 | Cholelithiasis | Occasional (29-5%) |
| HP:0001402 | Hepatocellular carcinoma | Occasional (29-5%) |
| HP:0001635 | Congestive heart failure | Occasional (29-5%) |
| HP:0001733 | Pancreatitis | Occasional (29-5%) |
| HP:0002027 | Abdominal pain | Occasional (29-5%) |
| HP:0002202 | Pleural effusion | Occasional (29-5%) |
| HP:0002608 | Celiac disease | Occasional (29-5%) |
| HP:0003073 | Hypoalbuminemia | Occasional (29-5%) |
| HP:0003459 | Polyclonal elevation of IgM | Occasional (29-5%) |
| HP:0003700 | Generalized amyotrophy | Occasional (29-5%) |
| HP:0004905 | Low levels of vitamin A | Occasional (29-5%) |
| HP:0008151 | Prolonged prothrombin time | Occasional (29-5%) |
| HP:0011892 | Low levels of vitamin K | Occasional (29-5%) |
| HP:0012115 | Hepatitis | Occasional (29-5%) |
| HP:0012378 | Fatigue | Occasional (29-5%) |
| HP:0030153 | Cholangiocarcinoma | Occasional (29-5%) |
| HP:0040275 | Adenocarcinoma of the large intestine | Occasional (29-5%) |
| HP:0100512 | Low levels of vitamin D | Occasional (29-5%) |
| HP:0100513 | Low levels of vitamin E | Occasional (29-5%) |
| HP:0100626 | Chronic hepatic failure | Occasional (29-5%) |
| HP:0100646 | Thyroiditis | Occasional (29-5%) |
| HP:0100651 | Type I diabetes mellitus | Occasional (29-5%) |
| HP:0000554 | Uveitis | Very rare (4-1%) |
| HP:0001298 | Encephalopathy | Very rare (4-1%) |
| HP:0006554 | Acute hepatic failure | Very rare (4-1%) |
| HP:0100575 | Neoplasm of the gallbladder | Very rare (4-1%) |
| HP:0001879 | Abnormal eosinophil morphology | Excluded (0%) |
| HP:0005429 | Recurrent systemic pyogenic infections | Excluded (0%) |
| HP:0011034 | Amyloidosis | Excluded (0%) |
| HP:0100727 | Histiocytosis | Excluded (0%) |
Total: 111
| HPO ID | Term | # of case reports |
|---|---|---|
| HP:0100279 | Ulcerative colitis | 88 |
| HP:0030151 | Cholangitis | 25 |
| HP:0001394 | Cirrhosis | 23 |
| HP:0030731 | Carcinoma | 19 |
| HP:0001396 | Cholestasis | 11 |
| HP:0012115 | Hepatitis | 11 |
| HP:0000952 | Jaundice | 9 |
| HP:0006280 | Chronic pancreatitis | 9 |
| HP:0006562 | Viral hepatitis | 8 |
| HP:0002583 | Colitis | 7 |
| HP:0002617 | Dilatation | 7 |
| HP:0000819 | Diabetes mellitus | 5 |
| HP:0000989 | Pruritus | 5 |
| HP:0001945 | Fever | 5 |
| HP:0001733 | Pancreatitis | 4 |
| HP:0001880 | Eosinophilia | 4 |
| HP:0002721 | Immunodeficiency | 4 |
| HP:0003003 | Colon cancer | 4 |
| HP:0005912 | Biliary atresia | 4 |
| HP:0200120 | Chronic active hepatitis | 4 |
| HP:0001369 | Arthritis | 3 |
| HP:0001399 | Hepatic failure | 3 |
| HP:0001406 | Intrahepatic cholestasis | 3 |
| HP:0002027 | Abdominal pain | 3 |
| HP:0002090 | Pneumonia | 3 |
| HP:0000099 | Glomerulonephritis | 2 |
| HP:0000112 | Nephropathy | 2 |
| HP:0001370 | Rheumatoid arthritis | 2 |
| HP:0001735 | Acute pancreatitis | 2 |
| HP:0001878 | Hemolytic anemia | 2 |
| HP:0002040 | Esophageal varix | 2 |
| HP:0002099 | Asthma | 2 |
| HP:0002586 | Peritonitis | 2 |
| HP:0002613 | Biliary cirrhosis | 2 |
| HP:0002664 | Neoplasm | 2 |
| HP:0002716 | Lymphadenopathy | 2 |
| HP:0002961 | Dysgammaglobulinemia | 2 |
| HP:0012378 | Fatigue | 2 |
| HP:0030242 | Portal vein thrombosis | 2 |
| HP:0032061 | Hypereosinophilia | 2 |
| HP:0100523 | Liver abscess | 2 |
| HP:0100646 | Thyroiditis | 2 |
| HP:0100806 | Sepsis | 2 |
| HP:0200123 | Chronic hepatitis | 2 |
| HP:0000100 | Nephrotic syndrome | 1 |
| HP:0000135 | Hypogonadism | 1 |
| HP:0000491 | Keratitis | 1 |
| HP:0000508 | Ptosis | 1 |
| HP:0000618 | Blindness | 1 |
| HP:0000821 | Hypothyroidism | 1 |
| HP:0000822 | Hypertension | 1 |
| HP:0000836 | Hyperthyroidism | 1 |
| HP:0000979 | Purpura | 1 |
| HP:0001009 | Telangiectasia | 1 |
| HP:0001081 | Cholelithiasis | 1 |
| HP:0001082 | Cholecystitis | 1 |
| HP:0001101 | Iritis | 1 |
| HP:0001405 | Periportal fibrosis | 1 |
| HP:0001408 | Bile duct proliferation | 1 |
| HP:0001409 | Portal hypertension | 1 |
| HP:0001695 | Cardiac arrest | 1 |
| HP:0001701 | Pericarditis | 1 |
| HP:0001824 | Weight loss | 1 |
| HP:0001903 | Anemia | 1 |
| HP:0001907 | Thromboembolism | 1 |
| HP:0002110 | Bronchiectasis | 1 |
| HP:0002196 | Myelopathy | 1 |
| HP:0002202 | Pleural effusion | 1 |
| HP:0002243 | Protein-losing enteropathy | 1 |
| HP:0002254 | Intermittent diarrhea | 1 |
| HP:0002570 | Steatorrhea | 1 |
| HP:0002638 | Superficial thrombophlebitis | 1 |
| HP:0002835 | Aspiration | 1 |
| HP:0002904 | Hyperbilirubinemia | 1 |
| HP:0002960 | Autoimmunity | 1 |
| HP:0003040 | Arthropathy | 1 |
| HP:0003124 | Hypercholesterolemia | 1 |
| HP:0003326 | Myalgia | 1 |
| HP:0003761 | Calcinosis | 1 |
| HP:0004420 | Arterial thrombosis | 1 |
| HP:0004947 | Arteriovenous fistula | 1 |
| HP:0005200 | Retroperitoneal fibrosis | 1 |
| HP:0005523 | Lymphoproliferative disorder | 1 |
| HP:0010450 | Esophageal stenosis | 1 |
| HP:0010783 | Erythema | 1 |
| HP:0011458 | Abdominal symptom | 1 |
| HP:0011838 | Sclerodactyly | 1 |
| HP:0012050 | Anasarca | 1 |
| HP:0012125 | Prostate cancer | 1 |
| HP:0012735 | Cough | 1 |
| HP:0025143 | Chills | 1 |
| HP:0025343 | Lupus anticoagulant | 1 |
| HP:0025520 | Calcinosis cutis | 1 |
| HP:0030154 | Gallbladder perforation | 1 |
| HP:0030167 | Antimitochondrial antibody positivity | 1 |
| HP:0030430 | Neuroma | 1 |
| HP:0030880 | Raynaud phenomenon | 1 |
| HP:0031274 | Hypovolemic shock | 1 |
| HP:0031281 | Sialadenitis | 1 |
| HP:0031690 | Opportunistic infection | 1 |
| HP:0031964 | Elevated serum alanine aminotransferase | 1 |
| HP:0032169 | Severe infection | 1 |
| HP:0032252 | Granuloma | 1 |
| HP:0040276 | Adenocarcinoma of the colon | 1 |
| HP:0100519 | Anuria | 1 |
| HP:0100537 | Fasciitis | 1 |
| HP:0100583 | Corneal perforation | 1 |
| HP:0100699 | Scarring | 1 |
| HP:0100749 | Chest pain | 1 |
| HP:0100762 | Hemobilia | 1 |
| HP:0200084 | Giant cell hepatitis | 1 |