Extraventricular neurocytoma

Extraventricular neurocytoma (EVN), a variant of central neurocytoma (see this term), is a rare neuronal neoplasm, composed of round cells with neuronal differentiation, which is located outside of the ventricular system, usually within the spinal cord or cerebral hemispheres and that manifests with headache, nausea, vomiting, complex partial seizures or focal neurological deficits. In some cases it may exhibit atypical features consistent with aggressive clinical behavior.



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Narrow down the case reports



Total: 43 (papers)

  


(per page)
Matched Phenotype  Gene  Mutation  MeSH
Rank
(Similarity)
PMID
(PMCID)
1
(35.3%)
30588667
Malignant progression of an extraventricular neurocytoma arising from the VIIIth cranial nerve: A case report and literature review.
Sugita Y, Furuta T, Komaki S, Ohshima K, Sakata K, Morioka M.
Neuropathology. 2019;39(2):120-126.
Facial palsy
GAB1 S100A1 SYP
Adult Brain Neoplasms Cranial Nerve Neoplasms Disease Progression Females Homo sapiens Neurocytoma
2
(4.0%)
30603610
Mesial temporal extraventricular neurocytoma (mtEVN): A case report and literature review.
Zhang A, Brown DF, Colpan EM.
Epilepsy Behav Case Rep. 2019;11:26-30.
Seizure
2
(4.0%)
29868519
(5958410)
Congenital Extra-Ventricular (Ganglio)Neurocytoma of the Brain Stem: A Case Report.
Piras M, Miele E, Di Giannatale A, Colafati GS, Diomedi-Camassei F, Vinci M, de Billy E, Mastronuzzi A, Carai A.
Front Pediatr. 2018;6:108.
Aggressive behavior
2
(4.0%)
29378347
Extraventricular Neurocytoma in the Left Frontal Lobe: A Case Report and Literature Review.
Chen F, Jin R, Wu X, Dong Z, Chen D.
World Neurosurg. 2018;112:178-181.
Urinary incontinence
MIB1 SYP
Brain Neoplasms Females Homo sapiens Magnetic Resonance Imaging Middle Aged Neurocytoma
2
(4.0%)
27597523
Progression of atypical extraventricular neurocytoma to anaplastic ganglioglioma.
Rusiecki D, Lach B, Manoranjan B, Fleming A, Ajani O, Singh SK.
Hum Pathol. 2017;59:125-130.
Neurocytoma
Biomarkers, Tumor Biopsy Brain Stem Neoplasms Cell Proliferation Child Disease Progression Fatal Outcome Females Ganglioglioma Homo sapiens Immunohistochemistry Infant Magnetic Resonance Imaging Neoplasm, Residual Neoplastic Cell Transformation Neurocytoma Time Factors
2
(4.0%)
27313678
(4888045)
Extraventricular neurocytoma in the left temporal lobe: A case report and review of the literature.
Ji YC, Hu JX, Li Y, Yan PX, Zuo HC.
Oncol Lett. 2016;11(6):3579-3582.
Headache
SYP
2
(4.0%)
26376790
(4574217)
Neurocytoma arising from a mature ovary teratoma: a case report.
Yu JH, Yang LH, Lin XY, Dai SD, Qiu XS, Wang EH.
Diagn Pathol. 2015;10:171.
Teratoma
GFAP RBFOX3 SYP
Biomarkers, Tumor Biopsy Females Homo sapiens Immunohistochemistry Neoplasms, Complex and Mixed Neurocytoma Teratoma X-Ray Computed Tomography Young Adult
2
(4.0%)
25608145
Extraventricular neurocytoma treated with 177Lu DOTATATE PRRT induction and maintenance therapies.
Makis W, McCann K, McEwan AJ.
Clin Nucl Med. 2015;40(3):234-6.
Headache
Females Homo sapiens Middle Aged Neurocytoma Organometallic Compounds Peptide Receptor Radiopharmaceuticals
2
(4.0%)
25524219
(4276055)
Behavioral disorders as unusual presentation of pediatric extraventricular neurocytoma: report on two cases and review of the literature.
Messina R, Cefalo MG, Secco DE, Cappelletti S, Rebessi E, Carai A, Colafati GS, Diomedi Camassei F, Cacchione A, Marras CE, Mastronuzzi A.
BMC Neurol. 2014;14:242.
Hyperactivity
Attention Deficit and Disruptive Behavior Disorder... Brain Neoplasms Child Homo sapiens Magnetic Resonance Imaging Male Neurocytoma
2
(4.0%)
24837842
[Atypical cerebellar neurocytoma resembling a hemangioblastoma. A case report].
Lista Martinez O, Rivas Lopez LA, Pombo Otero JF, Amaro Cendon S, Bravo Garcia C, Villa Fernandez JM.
Neurocirugia (Astur). 2014;25(4):189-93.
Neurocytoma
Cerebellar Neoplasms Differential Diagnosis Females Hemangioblastoma Homo sapiens Middle Aged Neurocytoma
        

Phenotype(s) retrieved from Orphanet

    Total: 0

HPO ID Term Frequency


Phenotype(s) retrieved from case reports

    Total: 9

HPO ID Term # of case reports
HP:0001250 Seizures 3
HP:0030064 Neurocytoma 2
HP:0000752 Hyperactivity 1
HP:0002013 Vomiting 1
HP:0002315 Headache 1
HP:0002539 Cortical dysplasia 1
HP:0002664 Neoplasm 1
HP:0008765 Auditory hallucinations 1
HP:0010302 Spinal cord tumor 1


Causative gene(s) retrieved from Orphanet

    Total: 0

Gene Symbol Gene Name Entrez Gene ID