Frontotemporal dementia, right temporal atrophy variant

Right temporal lobar atrophy (RTLA) is an anatomic variant of frontotemporal dementia (FTD), characterized by behavioral dysfunction, personality changes, episodic memory loss, and prosopagnosia; attributable to an asymmetrical predominantly right-sided, frontotemporal atrophy.



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Total: 0 (papers)
  


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Matched Phenotype  Gene  Mutation  MeSH
Rank
(Similarity)		 PMID
(PMCID)
        

Phenotype(s) retrieved from Orphanet

    Total: 23

HPO ID Term Frequency
HP:0002145 Frontotemporal dementia Very frequent (99-80%)
HP:0002354 Memory impairment Very frequent (99-80%)
HP:0000708 Behavioral abnormality Frequent (79-30%)
HP:0000710 Hyperorality Frequent (79-30%)
HP:0000734 Disinhibition Frequent (79-30%)
HP:0000737 Irritability Frequent (79-30%)
HP:0000741 Apathy Frequent (79-30%)
HP:0000745 Diminished motivation Frequent (79-30%)
HP:0000751 Personality changes Frequent (79-30%)
HP:0001300 Parkinsonism Frequent (79-30%)
HP:0002463 Language impairment Frequent (79-30%)
HP:0002591 Polyphagia Frequent (79-30%)
HP:0006892 Frontotemporal cerebral atrophy Frequent (79-30%)
HP:0008768 Inappropriate sexual behavior Frequent (79-30%)
HP:0010528 Prosopagnosia Frequent (79-30%)
HP:0012083 Ubiquitin-positive cerebral inclusion bodies Frequent (79-30%)
HP:0030902 Palmomental reflex Frequent (79-30%)
HP:0030904 Glabellar reflex Frequent (79-30%)
HP:0030905 Snout reflex Frequent (79-30%)
HP:0100543 Cognitive impairment Frequent (79-30%)
HP:0002367 Visual hallucinations Occasional (29-5%)
HP:0030018 Decreased female libido Occasional (29-5%)
HP:0040306 Decreased male libido Occasional (29-5%)


Phenotype(s) retrieved from case reports

    Total: 0

HPO ID Term # of case reports


Causative gene(s) retrieved from Orphanet

    Total: 0

Gene Symbol Gene Name Entrez Gene ID