Secondary sclerosing cholangitis

A rare, biliary tract disease characterized by development of sclerosing cholangitis due to a known primary insult to the biliary tree, including infections, autoimmune disease, exposure to toxic agents, obstructive and ischemic injuries. Patients may be initially asymptomatic with only elevated alkaline phosphatase and gamma glutamyltransferase levels. Later presentation includes abdominal pain, jaundice, pruritus, fever and bacterial cholangitis from ascending infection.



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Narrow down the case reports



Total: 42 (papers)

  


(per page)
Matched Phenotype  Gene  Mutation  MeSH
Rank
(Similarity)
PMID
(PMCID)
1
(23.3%)
23626514
(3617886)
Secondary Sclerosing Cholangitis due to Gallbladder Adenocarcinoma.
Fan DS, Sorser SA, Gamarra RM.
Case Rep Gastroenterol. 2013;7(1):134-9.
Cholestasis Low back pain
2
(17.5%)
25518767
Herniation of the liver: an extremely rare entity.
Tekin F, Arslan A, Gunsar F.
J Coll Physicians Surg Pak. 2014;24 Suppl 3:S186-7.
Cirrhosis Incisional hernia
Cholangitis, Sclerosing Females Homo sapiens Liver Liver Cirrhosis
2
(17.5%)
24831869
[Changing the therapeutic goal in critically ill patients. Ethical analysis of a surgical case].
Jox RJ, Ney L.
Unfallchirurg. 2014;117(5):399-405.
Shock Fasciitis
Adult Amputation Critical Illness Decision Making Decision Support Techniques Females Germany Homo sapiens Operative Surgical Procedures Patient Care Planning Patient-Centered Care Physician-Patient Relations Traumatology
4
(4.0%)
30861263
Secondary sclerosing cholangitis with hemobilia induced by pembrolizumab: Case report and review of published work.
Koya Y, Shibata M, Shinohara N, Nebuya S, Oe S, Honma Y, Senju M, Sato N, Harada M.
Hepatol Res. 2019;:.
Hemobilia
4
(4.0%)
30214777
(6132136)
Secondary sclerosing cholangitis following extracorporeal membrane oxygenation for acute respiratory distress in polytrauma.
Tunney R, Scott J, Rudralingam V, Liong S, Athwal VS.
Clin Case Rep. 2018;6(9):1849-1853.
Respiratory distress
4
(4.0%)
29484493
Secondary sclerosing cholangitis in critically ill patients after a traffic accident-a new entity that should be considered in death classification.
Zack F, Nizze H, Blaas V, Port A, Buttner A.
Int J Legal Med. 2018;132(6):1729-1732.
Hepatic encephalopathy
Cholangitis, Sclerosing Critical Illness Fatal Outcome Females Hepatic Encephalopathy Homo sapiens Liver Failure Middle Aged Multiple Trauma
4
(4.0%)
29331005
Pregnant Lady With Undiagnosed Hodgkin's Disease Presenting As Secondary Sclerosing Cholangitis.
Khattak T, Ali Shah SH, Khan W, Raza SS, Ahmad U, Ullah F.
J Ayub Med Coll Abbottabad. 2017;29(4):684-685.
Jaundice
Adult Cholangitis, Sclerosing Females Hodgkin Disease Homo sapiens Pregnancy Pregnancy Complications
4
(4.0%)
29179696
(5704558)
Secondary sclerosing cholangitis in localized hepatobiliary tuberculosis simulating cholangiocarcinoma: a rare case report.
Jain A, Chaturvedi R, Kantharia C, Joshi A, Londhe M, Kekan M.
BMC Gastroenterol. 2017;17(1):126.
Jaundice
Bile Duct Neoplasms Biliary Tract Diseases Cholangiocarcinoma Cholangitis, Sclerosing Differential Diagnosis Hepatectomy Homo sapiens Male Middle Aged Necrosis Tuberculosis, Hepatic
4
(4.0%)
28905689
IgG4-Related Cholangiopathy and Its Mimickers: A Case Report and Review Highlighting the Importance of Early Diagnosis.
Geary K, Yazici C, Seibold A, Guzman G.
Int J Surg Pathol. 2018;26(2):165-173.
Cholangitis
Autoimmune Diseases Cholangitis Differential Diagnosis Homo sapiens Male
4
(4.0%)
28620623
(5464395)
Resolution of Diffuse Intrahepatic Biliary Strictures after Chemotherapy for Metastatic Ovarian Cancer.
Lew D, Sundaram V, Barrows BD, Lo SK, Gaddam S.
ACG Case Rep J. 2017;4:e77.
Jaundice
        

Phenotype(s) retrieved from Orphanet

    Total: 0

HPO ID Term Frequency


Phenotype(s) retrieved from case reports

    Total: 10

HPO ID Term # of case reports
HP:0030151 Cholangitis 5
HP:0001082 Cholecystitis 1
HP:0001394 Cirrhosis 1
HP:0001409 Portal hypertension 1
HP:0002613 Biliary cirrhosis 1
HP:0002617 Dilatation 1
HP:0005575 Hemolytic-uremic syndrome 1
HP:0030987 Suppurative cholangitis 1
HP:0031690 Opportunistic infection 1
HP:0100762 Hemobilia 1


Causative gene(s) retrieved from Orphanet

    Total: 0

Gene Symbol Gene Name Entrez Gene ID