Wells syndrome

Wells syndrome is characterised by the presence of recurrent cellulitis-like eruptions with eosinophilia.



Input patient's signs and symptoms


Narrow down the case reports



Total: 107 (papers)

  


(per page)
Matched Phenotype  Gene  Mutation  MeSH
Rank
(Similarity)
PMID
(PMCID)
1
(42.2%)
2869073
Eosinophilic cellulitis associated with urticaria. A report of two cases.
Dijkstra JW, Bergfeld WF, Steck WD, Tuthill RJ.
J Am Acad Dermatol. 1986;14(1):32-8.
Recurrent sinusitis
Adult Biopsy Cellulitis Eosinophilia Histamine H1 Antagonists Homo sapiens Male Sinusitis Skin Urticaria
2
(38.6%)
9439777
Leptospirosis: twelve Turkish patients with the Weil syndrome.
Saltoglu N, Aksu HZ, Tasova Y, Arslan A, Canataroglu A, Dundar IH, Koksal F.
Acta Med Okayama. 1997;51(6):339-42.
Epistaxis Low back pain
Adult Females Homo sapiens Leptospira interrogans Leptospirosis Male Middle Aged Weil Disease
3
(36.8%)
2604023
Eosinophilic panniculitis associated with chronic recurrent parotitis.
Glass LA, Zaghloul AB, Solomon AR.
Am J Dermatopathol. 1989;11(6):555-9.
Parotitis Panniculitis
Adult Eosinophilia Females Homo sapiens Panniculitis Parotitis
4
(21.2%)
16490850
Eosinophilic cellulitislike reaction to subcutaneous etanercept injection.
Winfield H, Lain E, Horn T, Hoskyn J.
Arch Dermatol. 2006;142(2):218-20.
Edema Rheumatoid arthritis
CD8A
Antirheumatic Agents Biopsy Cellulitis Differential Diagnosis Eczema Eosinophilia Females Homo sapiens Middle Aged Recombinant Fusion Proteins Rheumatoid Arthritis Skin Subcutaneous Injections Tumor Necrosis Factor Receptor
4
(21.2%)
1083554
[Intermittent rheumatism revealing a familial syndrome. Arthritis--urticarian eruptions--deafness: Muckle-Wells syndrome without kidney amylosis].
Prost A, Barriere H, Legent F, Cottin S, Wallez B.
Rev Rhum Mal Osteoartic. 1976;43(3):201-8.
Arthritis
Adult Amyloidosis Child Child, Preschool Deafness Females Homo sapiens Kidney Diseases Male Middle Aged Pain Perceptual Disorders Rheumatism Syndrome Urticaria
6
(17.5%)
29469767
Eosinophilic infiltrate resembling eosinophilic cellulitis (Wells syndrome) in a patient with mycosis fungoides.
Emge DA, Lewis DJ, Aung PP, Duvic M.
Dermatol Online J. 2018;24(1):.
Hypereosinophilia Cellulitis
Aged, 80 and over Cellulitis Eosinophilia Fatal Outcome Homo sapiens Male Mycosis Fungoides Parotid Diseases Skin Neoplasms X-Ray Computed Tomography
6
(17.5%)
28951508
Wells syndrome associated with lung cancer.
Santos RP, Carvalho SD, Ferreira O, Brito C.
BMJ Case Rep. 2017;2017:.
Erythematous plaque Scarring
Administration, Topical Biopsy Cellulitis Dermatologic Agents Eosinophilia Homo sapiens Lung Neoplasms Male Middle Aged
6
(17.5%)
27839729
[Wells syndrome mimicking facial cellulitis: Three cases].
Gallard C, Law-Ping-Man S, Darrieux L, Tisseau L, Safa G.
Ann Dermatol Venereol. 2017;144(4):284-289.
Cellulitis
Adult Antipruritics Bacterial Infections Cellulitis Combination Drug Therapy Differential Diagnosis Eosinophilia Facial Dermatoses Females Homo sapiens Middle Aged
6
(17.5%)
27617724
Successful treatment of eosinophilic cellulitis with dapsone.
Coelho de Sousa V, Laureano Oliveira A, Cardoso J.
Dermatol Online J. 2016;22(7):.
Eosinophilia Cellulitis
Anti-Infective Agents Cellulitis Eosinophilia Females Homo sapiens Leg Dermatoses Middle Aged
6
(17.5%)
26586016
[Eosinophilic cellulitis: About a new pediatric case].
Makni S, Kallel R, Chaabene H, Bahloul E, Bahri I, Turki H, Gouiaa N, Boudawara T.
Ann Pathol. 2015;35(6):486-8.
Cellulitis
Adrenal Cortex Hormones Anti-Inflammatory Agents Cellulitis Eosinophilia Homo sapiens Infant Male Skin Diseases, Vesiculobullous
        

Phenotype(s) retrieved from Orphanet

    Total: 9

HPO ID Term Frequency
HP:0000989 Pruritus Very frequent (99-80%)
HP:0100658 Cellulitis Very frequent (99-80%)
HP:0000969 Edema Frequent (79-30%)
HP:0001880 Eosinophilia Frequent (79-30%)
HP:0008066 Abnormal blistering of the skin Frequent (79-30%)
HP:0200037 Skin vesicle Frequent (79-30%)
HP:0001945 Fever Occasional (29-5%)
HP:0002829 Arthralgia Occasional (29-5%)
HP:0002633 Vasculitis Excluded (0%)


Phenotype(s) retrieved from case reports

    Total: 39

HPO ID Term # of case reports
HP:0001880 Eosinophilia 17
HP:0100658 Cellulitis 16
HP:0010783 Erythema 9
HP:0000969 Edema 4
HP:0025084 Folliculitis 3
HP:0001945 Fever 2
HP:0002099 Asthma 2
HP:0003201 Rhabdomyolysis 2
HP:0012490 Panniculitis 2
HP:0025474 Erythematous plaque 2
HP:0032061 Hypereosinophilia 2
HP:0032282 Contact dermatitis 2
HP:0000952 Jaundice 1
HP:0000989 Pruritus 1
HP:0001025 Urticaria 1
HP:0001047 Atopic dermatitis 1
HP:0001433 Hepatosplenomegaly 1
HP:0001482 Subcutaneous nodule 1
HP:0001873 Thrombocytopenia 1
HP:0002113 Pulmonary infiltrates 1
HP:0002716 Lymphadenopathy 1
HP:0002829 Arthralgia 1
HP:0002840 Lymphadenitis 1
HP:0002860 Squamous cell carcinoma 1
HP:0004322 Short stature 1
HP:0011947 Respiratory tract infection 1
HP:0012115 Hepatitis 1
HP:0012224 Circulating immune complexes 1
HP:0012344 Morphea 1
HP:0012393 Allergy 1
HP:0012733 Macule 1
HP:0030351 Urticarial plaque 1
HP:0030828 Wheezing 1
HP:0032252 Granuloma 1
HP:0040276 Adenocarcinoma of the colon 1
HP:0100279 Ulcerative colitis 1
HP:0100699 Scarring 1
HP:0100758 Gangrene 1
HP:0200119 Acute hepatitis 1


Causative gene(s) retrieved from Orphanet

    Total: 0

Gene Symbol Gene Name Entrez Gene ID