Pulmonary atresia with ventricular septal defect

Pulmonary atresia with ventricular septal defect (PA-VSD) is a rare cyanotic congenital heart malformation characterized by underdevelopment of the right ventricular outflow tract and atresia of the pulmonary valve, ventricular septal defect (VSD) and pulmonary collateral vessels. Clinical features depend on the anatomic variability of the lesion and patients may be minimally symptomatic, severely cyanotic or may develop congestive heart failure. PA-VSD may represent a severe form of Tetralogy of Fallot (see this term).

Coronary-pulmonary artery fistula

A congenital malformation with abnormal connection between one of the coronary arteries and the pulmonary artery.

Total: 2

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PMID (PMCID)
30764888	FEMALE	Infant, Newborn
	Utilisation of a three-dimensional printed model for the management of coronary-pulmonary artery fistula from left main coronary artery.
	Misra A, Walters HL, Kobayashi D. Cardiol Young. 2019;29(3):431-434.
	Coronary-pulmonary artery fistula is a rare anomaly in which an aortopulmonary collateral artery arises from a coronary artery, often seen in patients with pulmonary atresia with ventricular septal defect.
28496023	MALE	Infant, Newborn
	Bilateral Coronary-Pulmonary Artery Fistulas in Pulmonary Atresia With Ventricular Septal Defect.
	Nagatomo Y, Muneuchi J, Watanabe M, Joo K, Ochiai Y. Int Heart J. 2017;58(3):463-465.
	Bilateral Coronary-Pulmonary Artery Fistulas in Pulmonary Atresia With Ventricular Septal Defect.