Progressive hemifacial atrophy

Progressive hemifacial atrophy (PHA) is a rare acquired disorder, characterized by unilateral slowly progressive atrophy of the skin and soft tissues of half of the face leading to a sunken appearance. Muscles, cartilage and the underlying bony structures may also be involved.

Morphea

Isolated patches of hardened skin (scleroderma).


Total: 15

                      


(per page)
PMID (PMCID)
30213201
OTHER
Facial solitary morphea profunda presenting with painful trigeminal neuropathy: A case report.
Moreno-Ajona D, Moreno-Artero E, Garcia de Eulate MR, Irimia P, Espana A.
Cephalalgia. 2019;39(4):564-568.
Localized facial scleroderma usually presents as frontal linear morphea or progressive hemifacial atrophy.
29380800
(5819137)
FEMALE
An overlap case of Parry-Romberg syndrome and en coup de sabre with striking ocular involvement and anti-double-stranded DNA positivity.
Atas H, Gonul M, Gokce A, Acar M, Gurdal C.
Indian J Ophthalmol. 2018;66(2):336-338.
Parry-Romberg syndrome (PRS) may overlap localized scleroderma (morphea) lesions with linear depression (en coup de sabre [ECDS]).
29849855
(5966626)
OTHER
Neuroimaging and clinical findings in a case of linear scleroderma en coup de sabre.
Duman IE, Ekinci G.
Radiol Case Rep. 2018;13(3):545-548.
En coup de sabre and Parry-Romberg syndrome are variants of linear morphea on the head and neck that can be associated with neurologic manifestations.
27776552
(5078903)
MIXED_SAMPLE Young Adult
Scleroderma and dentistry: Two case reports.
Dixit S, Kalkur C, Sattur AP, Bornstein MM, Melton F.
J Med Case Rep. 2016;10(1):297.
Hence, our final diagnosis was mixed morphea with Parry-Romberg syndrome.
27776552
(5078903)
MIXED_SAMPLE Young Adult
Scleroderma and dentistry: Two case reports.
Dixit S, Kalkur C, Sattur AP, Bornstein MM, Melton F.
J Med Case Rep. 2016;10(1):297.
Hence, we present a case of morphea, associated with Parry-Romberg syndrome, and a second case with the classical signs of progressive systemic sclerosis.
27776552
(5078903)
MIXED_SAMPLE Young Adult
Scleroderma and dentistry: Two case reports.
Dixit S, Kalkur C, Sattur AP, Bornstein MM, Melton F.
J Med Case Rep. 2016;10(1):297.
Morphea can manifest itself as hemifacial atrophy (Parry-Romberg syndrome) although this remains debatable.
27776552
(5078903)
MIXED_SAMPLE Young Adult
Scleroderma and dentistry: Two case reports.
Dixit S, Kalkur C, Sattur AP, Bornstein MM, Melton F.
J Med Case Rep. 2016;10(1):297.
Morphea can manifest itself as hemifacial atrophy (Parry-Romberg syndrome) although this remains debatable.
25136439
(4134867)
OTHER
Parry Romberg syndrome with localized scleroderma: A case report.
Khan M, Khan M, Negi R, Gupta N.
J Clin Exp Dent. 2014;6(3):e313-6.
Key words: Parry Romberg syndrome, progressive facial hemiatrophy, morphea, localized scleroderma.
25136439
(4134867)
OTHER
Parry Romberg syndrome with localized scleroderma: A case report.
Khan M, Khan M, Negi R, Gupta N.
J Clin Exp Dent. 2014;6(3):e313-6.
Key words: Parry Romberg syndrome, progressive facial hemiatrophy, morphea, localized scleroderma.
24365008
FEMALE Adult
Hemifacial atrophy.
Vedvyas C, Urbanek RW.
Dermatol Online J. 2013;19(12):20717.
We report the case of a 44-year-old woman with a one-year history of en coup de sabre morphea and progressive hemifacial atrophy with ipsilateral hemifacial neuralgia, migraine, and contralateral neurologic abnormalities.
22535610
FEMALE
Pemphigoid gestationis in a female with progressive facial hemiatrophy: microchimerism as a speculative shared background is disputable.
Pietkiewicz P, Gornowicz-Porowska J, Bowszyc-Dmochowska M, Dmochowski M.
Pol J Pathol. 2012;63(1):71-4.
Here, the first report on coexistence of pregnancy-associated pemphigoid gestationis (PG) and progressive facial hemiatrophy, a form of "en coup de sabre" morphea, is presented.
21550692
MIXED_SAMPLE Child
Activity assessment in morphea using color Doppler ultrasound.
Wortsman X, Wortsman J, Sazunic I, Carreno L.
J Am Acad Dermatol. 2011;65(5):942-8.
Five of the patients had the Parry-Romberg syndrome with ipsilateral parotid gland inflammatory involvement, and one had an asymptomatic but sonographically active morphea lesion.
20671858
(2905582)
OTHER
Parry-Romberg Syndrome Associated with Localized Scleroderma.
Maletic J, Tsirka V, Ioannides P, Karacostas D, Taskos N.
Case Rep Neurol. 2010;2(2):57-62.
We present a case of Parry-Romberg syndrome with neurological involvement in a patient with diagnosed localized scleroderma (morphea).
19061620
FEMALE
Parry-Romberg syndrome with coexistent morphea.
Lane TK, Cheung J, Schaffer JV.
Dermatol Online J. 2008;14(10):21.
Parry-Romberg syndrome with coexistent morphea.
19061620
FEMALE
Parry-Romberg syndrome with coexistent morphea.
Lane TK, Cheung J, Schaffer JV.
Dermatol Online J. 2008;14(10):21.
This case highlights the substantial of overlap of Parry-Romberg syndrome and morphea.