Progressive hemifacial atrophy

Progressive hemifacial atrophy (PHA) is a rare acquired disorder, characterized by unilateral slowly progressive atrophy of the skin and soft tissues of half of the face leading to a sunken appearance. Muscles, cartilage and the underlying bony structures may also be involved.

Hemiatrophy

Undergrowth of the limbs that affects only one side.


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PMID (PMCID)
30739340
 MIXED_SAMPLE Child
Botulinum toxin A for pain reduction in pediatric patients with Parry-Romberg syndrome.
Mishra K, Sood A, Smidt A, Price HN.
Pediatr Dermatol. 2019;36(2):223-226.
Parry-Romberg syndrome (PRS) is characterized by hemiatrophy of facial structures, including skin, subcutaneous fat, muscle, bone, and cartilage.
30429134
 FEMALE Middle Aged
Parry-Romberg syndrome in a patient with scleroderma.
Kuah CY, Koleva E, Gan JJL, Iqbal T.
BMJ Case Rep. 2018;2018:.
Parry-Romberg syndrome (PRS) is characterised by progressive but self-limiting facial hemiatrophy.
26335318
 MALE Child
New and Successful Technique for the Management of Parry-Romberg Syndrome's Soft Tissue Atrophy.
Ortega VG, Sastoque D.
J Craniofac Surg. 2015;26(6):e507-10.
Parry-Romberg syndrome (PRS) is an infrequent, acquired disorder characterized by progressive hemiatrophy of the skin and soft tissue of the face and, in some patients, results in atrophy of muscles, cartilage, and the underlying bony structures.The disease process exhibits varying speeds of development, with onset occurring in early infancy or adolescence.
22149072
 FEMALE Adult
Ocular motor dysfunction in Parry-Romberg syndrome: four cases.
Prescott CR, Hasbani MJ, Levada AJ, Silbert JE, Winterkorn JM, Lesser RL.
J Pediatr Ophthalmol Strabismus. 2011;48 Online:e63-6.
The authors describe four patients with Parry-Romberg syndrome (PRS) who had abnormal eye movements, ptosis, and facial hemiatrophy.
19969487
 FEMALE Adult
Use of autologous fat graft for correction of facial asymmetry stemming from Parry-Romberg syndrome.
Avelar RL, Goelzer JG, Azambuja FG, de Oliveira RB, de Oliveira MP, Pase PF.
Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2010;109(2):e20-5.
Facial hemiatrophy is a typical manifestation of Parry-Romberg syndrome, characterized by a slow progressive atrophy that appears in early stages of life, primarily affecting the subcutaneous tissue and subjacent fat on 1 side of the face.
20465894
 OTHER
Giant intracranial aneurysm in a ten-year-old boy with parry romberg syndrome. A case report and literature review.
Bosman T, Van Bei Jnum J, Van Walderveen MA, Brouwer PA.
Interv Neuroradiol. 2009;15(2):165-73.
Parry-Romberg syndrome (PRS) is a rare acquired syndrome consisting of progressive hemiatrophy of the face.We present a child with PRS and progressive neurological deficit caused by a giant intracranial aneurysm and reviewed the literature concerning all intracranial abnormalities in patients with PRS.A literature search identified 27 articles reporting on 88 patients ith PRS and intracranial abnormalities.
19093144
 FEMALE Young Adult
Minimally invasive combined treatment for Parry-Romberg syndrome.
Onesti MG, Monarca C, Rizzo MI, Mazzocchi M, Scuderi N.
Aesthetic Plast Surg. 2009;33(3):452-6.
Facial hemiatrophy, a typical manifestation of Parry-Romberg syndrome, produces massive face asymmetry, causing marked aesthetic damage and severe psychological discomfort, with repercussions to the psychophysical status of the patient.
11744320
 MALE
Parry-Romberg syndrome associated with Adie's pupil and radiologic findings.
Aynaci FM, Sen Y, Erdol H, Ahmetoglu A, Elmas R.
Pediatr Neurol. 2001;25(5):416-8.
We describe Adie's pupil and radiologic changes related to Parry-Romberg syndrome in a child who presented with facial hemiatrophy with no neurologic deficit.
9127045
 FEMALE
Clinical and radiologic findings in progressive facial hemiatrophy (Parry-Romberg syndrome).
Cory RC, Clayman DA, Faillace WJ, McKee SW, Gama CH.
AJNR Am J Neuroradiol. 1997;18(4):751-7.
We describe the clinical and radiologic changes related to progressive facial hemiatrophy (Parry-Romberg syndrome) occurring during a 20-month period in a child who presented with unilateral neurologic deficits and facial hemiatrophy.
9127045
 FEMALE
Clinical and radiologic findings in progressive facial hemiatrophy (Parry-Romberg syndrome).
Cory RC, Clayman DA, Faillace WJ, McKee SW, Gama CH.
AJNR Am J Neuroradiol. 1997;18(4):751-7.
We describe the clinical and radiologic changes related to progressive facial hemiatrophy (Parry-Romberg syndrome) occurring during a 20-month period in a child who presented with unilateral neurologic deficits and facial hemiatrophy.
1646532
 FEMALE Adult
[Facial hemiatrophy (Parry-Romberg syndrome)].
Poliakova NF, Lebezeva IV, Kisel' SA, Oknin VIu.
Zh Nevropatol Psikhiatr Im S S Korsakova. 1991;91(3):28-9.
[Facial hemiatrophy (Parry-Romberg syndrome)].
2097359
 FEMALE Child
Duane's retraction syndrome with facial hemiatrophy (a case report).
Sharma DC, Parihar PS, Kumawat DC, Ramakrishnan S, Dave R, Bhatnagar HN, Bhatnagar LK.
J Postgrad Med. 1990;36(1):51-3.
This report deals with a young girl with Duane's retraction syndrome who also had left facial hemiatrophy (Parry-Romberg syndrome).
2930126
 FEMALE Child
["Saber-cut" scleroderma and Parry-Romberg facial hemiatrophy. Nosologic problems. Neurologic complications].
Klene C, Massicot P, Ferriere-Fontan I, Sarlangue J, Fontan D, Guillard JM.
Ann Pediatr (Paris). 1989;36(2):123-5.
We report two cases of gradual facial hemiatrophy (Parry-Romberg syndrome).
28193932
 OTHER
Localized Scleroderma (case Report of 23 Cases).
Reddy BS, Singh G.
Indian J Dermatol Venereol Leprol. 1982;48(5):276-281.
It is felt important to differentiate between the facial hemiatrophy associated with en coup de, sabre and Romberg's syndrome (progressive facial hemiatrophy).
7167694
 FEMALE Adult
[Scleroderma with progressive facial hemiatrophy and atrophy of the other side of the body].
Lapresle J, Desi M.
Rev Neurol (Paris). 1982;138(11):815-25.
The relationship between sclerodermic facial hemiatrophy and Parry Romberg syndrome are then discussed: the study of this case and the literature do not provide sufficient criteria to allow description of two separate entities.