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Budd-Chiari syndrome

Budd-Chiari syndrome (BCS) is caused by obstruction of hepatic venous outflow involving either the hepatic veins or the terminal segment of the inferior vena cava.

Jaundice

Yellow pigmentation of the skin due to bilirubin, which in turn is the result of increased bilirubin concentration in the bloodstream.

Total: 6

(per page)

PMID (PMCID)
31145318	MALE	Adult
	Transient Budd-Chiari syndrome as an unpredictable complication of supradiaphragmatic inferior vena cava reconstruction after blunt thoracic trauma: A case report.
	Kim JH, Baek JH. Medicine (Baltimore). 2019;98(22):e15821.
	Budd-Chiari syndrome (BCS) is also rare and presents with ascites, abdominal pain, hepatomegaly, leg swelling, and jaundice.
24584043	OTHER
	Living donor liver transplantation with replacement of vena cava for Echinococcus alveolaris: A case report.
	Mamedov R, Novruzov N, Baskiran A, Yetisir F, Unal B, Aydn C, Bayramov N, Kayaalp C, Yilmaz S. Int J Surg Case Rep. 2014;5(3):169-71.
	Advanced stage of AED like chronic jaundice, liver abscess, sepsis, repeated attacks of cholangitis, portal hypertension, and Budd-Chiari syndrome may be an indication for liver transplantation.
23971776	FEMALE	Adult
	Bilateral lower limb edema caused by compression of the retrohepatic inferior vena cava by a giant hepatic hemangioma.
	Akbulut S, Yilmaz M, Kahraman A, Yilmaz S. Int Surg. 2013;98(3):229-33.
	In a very small minority of patients, nausea, vomiting, abdominal pain, distension, palpable mass, obstructive jaundice, bleeding, and signs and symptoms of Budd-Chiari syndrome may develop due to compression of bile duct, hepatic vein, portal vein, and adjacent organs.
19386569	FEMALE	Adult
	[Surgical treatment of primary leiomyosarcoma of the inferior vena cava].
	Biro ZJ, Kalmar Nagy K, Feher E, Gomori E, Horvath OP. Magy Seb. 2009;62(2):83-6.
	Upper segment tumours can cause Budd-Chiari syndrome (hepatomegaly, abdominal pain, jaundice and ascites) with a bad prognosis.
16517788	MIXED_SAMPLE	Adult
	Catheter-directed thrombolysis and thrombectomy for the Budd-Chiari syndrome in paroxysmal nocturnal hemoglobinuria in three patients.
	Kuo GP, Brodsky RA, Kim HS. J Vasc Interv Radiol. 2006;17(2 Pt 1):383-7.
	Patients with hepatic vein thrombosis (Budd-Chiari syndrome) can present with abdominal pain, hepatomegaly, jaundice, and ascites.
14989119	FEMALE	Adult
	Allopurinol hypersensitivity syndrome as a cause of hepatic centrilobular hemorrhagic necrosis.
	Mete N, Yilmaz F, Gulbahar O, Aydin A, Sin A, Kokuludag A, Yuce G, Sebik F. J Investig Allergol Clin Immunol. 2003;13(4):281-3.
	Here we report a case of a 41-year-old female who developed fever, pruritic skin rash, jaundice, eosinophilia, abnormal liver function tests, and acute renal failure 3 weeks after the beginning of allopurinol treatment, complicated with severe hepatocyte necrosis around most terminal hepatic venules suggesting Budd-Chiari syndrome.