Budd-Chiari syndrome

Budd-Chiari syndrome (BCS) is caused by obstruction of hepatic venous outflow involving either the hepatic veins or the terminal segment of the inferior vena cava.

Cirrhosis

A chronic disorder of the liver in which liver tissue becomes scarred and is partially replaced by regenerative nodules and fibrotic tissue resulting in loss of liver function.


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(per page)
PMID (PMCID)
31163972
 OTHER
Use of idarucizumab in clinical practice: acase report.
Husova L.
Vnitr Lek. 2019;65(5):377-378.
Budd-Chiari syndrome is aserious condition which in chronic course leads to the development of liver cirrhosis.
31049175
 OTHER
A High Serum-Ascites Albumin Gradient and Mediastinal Fibrosarcoma: A Case Report.
Hormati A, Jameshorani M, Sarkeshikian S, Ghadir MR, Alemi F.
Middle East J Dig Dis. 2018;10(4):258-262.
This condition has some differential diagnoses such as liver cirrhosis, Budd-Chiari syndrome, heart failure, and idiopathic portal fibrosis.
29528017
 MALE Young Adult
Budd-Chiari Syndrome Diagnosed in a Patient Listed for Liver Transplant and Considered to be Contraindicated for the Operation.
Yesmembetov K, Muratova Z, Borovskiy S, Ten I, Kaliaskarova K.
Exp Clin Transplant. 2018;16 Suppl 1(Suppl 1):158-161.
Therefore, considering preserved liver function and severe portal hypertension, diagnosis of Budd-Chiari syndrome with subsequent development of liver cirrhosis was made.
30305603
(6196583)
 FEMALE
Hepatic Involvement in Systemic Sarcoidosis.
Ibrahim AM, Bhandari B, Soriano PK, Quader Z, Gao JZ, Shuster D, Mamillapalli CK.
Am J Case Rep. 2018;19:1212-1215.
In rare cases, hepatic sarcoidosis can lead to cholestasis, portal hypertension, cirrhosis, or Budd-Chiari syndrome.
28604464
 FEMALE Adult
Liver Transplantation in a Patient With Antiphospholipid Syndrome: A Case Report.
Steckelberg RC, Antongiorgi ZD, Steadman RH.
A A Case Rep. 2017;9(5):148-150.
We present a patient with a history of APS, Budd-Chiari syndrome with cirrhosis, hepatopulmonary syndrome, and heparin-induced thrombocytopenia who underwent liver transplantation complicated by hepatic artery thrombosis.
27746432
(5109562)
 MALE Middle Aged
Successful Treatment of Ascites using a Denver Peritoneovenous Shunt in a Patient with Paroxysmal Nocturnal Hemoglobinuria and Budd-Chiari syndrome.
Kogiso T, Hashimoto E, Ito T, Hara T, Ikarashi Y, Kodama K, Taniai M, Torii N, Yoshinaga K, Morita S, Takahashi Y, Tanaka J, Sakai S, Yamamoto M, Tokushige K.
Intern Med. 2016;55(20):2957-2963.
Liver cirrhosis, ascites, and thrombus in the hepatic veins were found at 56 years of age and Budd-Chiari syndrome (BCS) was diagnosed according to angiography findings.
26552285
 MALE Adult
Budd-Chiari Syndrome in a patient with Multiple Hypercoagulopathies.
Kraleti S.
J Ark Med Soc. 2015;112(6):90-1.
A 33-year-old man who presented with abdominal distension, hematemesis, shortness of breath was found to have liver cirrhosis, portal hypertension and Budd-Chiari Syndrome.
26191114
(4501637)
 OTHER
Membranous IVC Obstruction Presenting with Antegrade/Retrograde Respiratory Flow in the Intrahepatic Segment in Doppler Imaging and Prostatic and Urethral Congestion.
Sood D, Mistry KA, Chadha V, Sharma S, Morey PD, Suthar PP, Patel DG.
Pol J Radiol. 2015;80:350-5.
Early diagnosis is important, as it can lead to hepatic congestion, cirrhosis and Budd-Chiari syndrome (BCS) and can predispose to development of hepatocellular carcinoma (HCC) in severe cases.
24727524
 FEMALE Adult
Hepatic encephalomyelopathy: a complication following liver cirrhosis caused by Budd-Chiari syndrome and HBV.
Cheng J, Jiang SW, Zhou ZS, Sun QL.
J Infect Dev Ctries. 2014;8(4):551-3.
Hepatic encephalomyelopathy: a complication following liver cirrhosis caused by Budd-Chiari syndrome and HBV.
24727524
 FEMALE Adult
Hepatic encephalomyelopathy: a complication following liver cirrhosis caused by Budd-Chiari syndrome and HBV.
Cheng J, Jiang SW, Zhou ZS, Sun QL.
J Infect Dev Ctries. 2014;8(4):551-3.
The case of a patient with hepatic encephalomyelopathy associated with Budd-Chiari syndrome and HBV-related cirrhosis is presented.
23997080
 MALE Adult
A novel subtype of myeloproliferative disorder? JAK2V617F-associated hypereosinophilia with hepatic venous thrombosis.
Dasari S, Naha K, Hande M, Vivek G.
BMJ Case Rep. 2013;2013:.
An evaluation revealed hepatic cirrhosis with portal hypertension, secondary to chronic Budd-Chiari syndrome.
23769108
 MALE Middle Aged
Case report: maximum-intensity projection and minimum-intensity projection of computed tomography are helpful in the diagnosis of Budd-Chiari syndrome in complicated liver cirrhosis.
Jeng KS, Huang CC, Lin CK, Lin CC, Chen KH.
Transplant Proc. 2013;45(5):2059-62.
Case report: maximum-intensity projection and minimum-intensity projection of computed tomography are helpful in the diagnosis of Budd-Chiari syndrome in complicated liver cirrhosis.
23622659
 MIXED_SAMPLE Child
Vascular complications after orthotopic liver transplantation in Estonia.
Vali T, Tein A, Tiganik V, Ulst K.
Transplant Proc. 2013;45(3):1201-3.
Their diagnoses were cholestatic disease (n = 8); hepatitis C virus (HCV) cirrhosis (n = 6); tumor (n = 3); Budd-Chiari syndrome (n = 2); autoimmune hepatitis (n = 1); cystic fibrosis (n = 1); or fulminant hepatic failure (n = 1).
22681996
 MALE Middle Aged
[Chronic Budd-Chiari syndrome can cause liver cirrhosis].
Karlsen S, Nielsen DT, Gronbaek H.
Ugeskr Laeger. 2012;174(24):1677-9.
[Chronic Budd-Chiari syndrome can cause liver cirrhosis].
21668639
 MALE Adult
Left renal vein ligation: a technique to mitigate low portal flow from splenic vein siphon during liver transplantation.
Slater RR, Jabbour N, Abbass AA, Patil V, Hundley J, Kazimi M, Kim D, Yoshida A, Abouljoud M.
Am J Transplant. 2011;11(8):1743-7.
The patient is a 43-year-old male with cirrhosis from hepatitis C and Budd-Chiari syndrome, who had a variceal hemorrhage necessitating an emergent splenorenal shunt with 8 mm PTFE graft.
20387679
 MALE Middle Aged
[A case of chronic Budd-Chiari syndrome].
Zheltova OI, Batorov EV, Starostina NM.
Ter Arkh. 2010;82(2):56-9.
The paper describes a long (more than 20 years) course of the Budd-Chiari syndrome in which only a special angiographic study could verify the presumptive diagnosis and reveal the cause of evolving liver cirrhosis.
18328792
 FEMALE Middle Aged
Undiagnosed myeloproliferative disease in cases of intra-abdominal thrombosis: the utility of the JAK2 617F mutation.
P'ng S, Carnley B, Baker R, Kontorinis N, Cheng W.
Clin Gastroenterol Hepatol. 2008;6(4):472-5.
Extrahepatic portal vein thrombosis and Budd-Chiari syndrome frequently result from multiple concurrent factors such as cirrhosis, intra-abdominal sepsis, procoagulant states, and underlying myeloproliferative disorders (MPDs).
19058526
 FEMALE Adult
[Budd-Chiari syndrome induced by hormonal oral contraception in the patient with congenital thrombophilia-factor V Leiden mutation--a case report].
Samborek M, Drosdzol A, Stojko R, Wilk K, Witek A.
Ginekol Pol. 2008;79(10):702-5.
Liver cirrhosis, malignant tumors and haematological disorders resulting in hypercoagulability, are the most common reasons of Budd-Chiari syndrome.
17249502
(3891025)
 MIXED_SAMPLE Adult
Diagnostic usefulness of the Janus kinase 2 mutation in non BCR/ABL myeloproliferative disorders.
Bang SM, Ahn JY, Park J, Yoo SJ, Park SH, Nam EM, Park PW, Seo YH, Cho EK, Shin DB, Lee JH.
Korean J Intern Med. 2006;21(4):219-24.
These patients had liver cirrhosis and hypersplenism due to Budd-Chiari syndrome (1), gastrointestinal bleeding (1) or the initial hemoglobin level was slightly below the level as provided by the criteria, but the level showed a rising pattern despite cytoreductive therapy (2).
15660176
 MIXED_SAMPLE Middle Aged
Cryptococcus neoformans peritonitis in two patients with liver cirrhosis.
Jean SS, Wang JL, Wang JT, Fang CT, Chen YC, Chang SC.
J Formos Med Assoc. 2005;104(1):39-42.
Patient 2, a 51-year-old woman with liver cirrhosis due to Budd-Chiari syndrome, had C. neoformans isolated from ascites, cerebrospinal fluid, and blood culture.