Budd-Chiari syndrome

Budd-Chiari syndrome (BCS) is caused by obstruction of hepatic venous outflow involving either the hepatic veins or the terminal segment of the inferior vena cava.

Hepatic failure



Total: 6

                       


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PMID (PMCID)
24724450
 MALE Adult
[Case of brain death liver transplantation suspended because of respiratory failure after admission to the operating room].
Hatakeyama T, Nagata H, Miura H, Inoda A, Suzuki T, Suzuki K.
Masui. 2014;63(3):350-2.
A 32-year-old man (weight 70 kg, height 164 cm) who had previously undergone living donor liver transplantation for Budd-Chiari syndrome developed hepatic failure 11 months after the transplantation and was enrolled in the waiting list for brain death liver transplantation.
23210433
(3514094)
 OTHER
Eculizumab in paroxysmal nocturnal hemoglobinuria with Budd-Chiari syndrome progressing despite anticoagulation.
Brodsky A, Mazzocchi O, Sanchez F, Khursigara G, Malhotra S, Volpacchio M.
Exp Hematol Oncol. 2012;1(1):26.
This case shows that terminal complement blockade with eculizumab can reverse progressive thromboses and hepatic failure that is unresponsive to anticoagulation therapy and suggests that early initiation of eculizumab should be included in the therapeutic regimen of patients with PNH-related Budd-Chiari syndrome.
11951701
 FEMALE
Fulminate intracardiac thrombosis associated with Budd-Chiari-syndrome and inferior vena cava thrombosis.
Eckel F, Huber W, Heidecke CD, Moessmer G, Berger H, Holper K, Dietrich W, Lersch C, Siewert JR.
Vasa. 2002;31(1):62-5.
Hepatic failure due to venous outflow obstruction (Budd-Chiari syndrome, BCS) was diagnosed.
2387522
 FEMALE Adult
Acute Budd-Chiari syndrome with hepatic failure and obstruction of the inferior vena cava as presenting manifestations of hereditary protein C deficiency.
Bourliere M, Le Treut YP, Arnoux D, Castellani P, Bordigoni L, Maillot A, Antoni M, Botta D, Pol B, Gauthier AP.
Gut. 1990;31(8):949-52.
Acute Budd-Chiari syndrome with hepatic failure and obstruction of the inferior vena cava as presenting manifestations of hereditary protein C deficiency.
2652979
 FEMALE Adult
Primary leiomyosarcoma of the inferior vena cava with Budd-Chiari syndrome.
Imakita M, Yutani C, Ishibashi-Ueda H, Hiraoka H, Naito H.
Acta Pathol Jpn. 1989;39(1):73-7.
She presented with Budd-Chiari syndrome and died of hepatic failure about 3 months after the onset of symptoms.
3287665
 MIXED_SAMPLE Adult
Hepatic transplantation with perioperative and long term anticoagulation as treatment for Budd-Chiari syndrome.
Campbell DA Jr, Rolles K, Jamieson N, O'Grady J, Wight D, Williams R, Calne R.
Surg Gynecol Obstet. 1988;166(6):511-8.
Despite the difficulties in patient management, a carefully selected population of patients with hepatic failure secondary to Budd-Chiari syndrome appear to be well served by hepatic transplantation with early postoperative and long term anticoagulant therapy.