Budd-Chiari syndrome

Budd-Chiari syndrome (BCS) is caused by obstruction of hepatic venous outflow involving either the hepatic veins or the terminal segment of the inferior vena cava.

Hypersplenism

A malfunctioning of the spleen in which it prematurely destroys red blood cells.


Total: 3

                       


(per page)
PMID (PMCID)
27757214
(5062621)
 OTHER
Positive Impact of Eculizumab Therapy on Surgery for Budd-Chiari Syndrome in a Patient with Paroxysmal Nocturnal Hemoglobinuria and a Long-Term History of Thrombosis.
De-la-Iglesia S, Luzardo H, Lemes A, Torres M, Gomez-Casares MT, Cruz N, Molero T.
Hematol Rep. 2016;8(3):6562.
We report the case of a 46-year-old male with PNH who presented with Budd-Chiari syndrome associated with portal cavernoma, portal hypertension and hypersplenism.
17249502
(3891025)
 MIXED_SAMPLE Adult
Diagnostic usefulness of the Janus kinase 2 mutation in non BCR/ABL myeloproliferative disorders.
Bang SM, Ahn JY, Park J, Yoo SJ, Park SH, Nam EM, Park PW, Seo YH, Cho EK, Shin DB, Lee JH.
Korean J Intern Med. 2006;21(4):219-24.
These patients had liver cirrhosis and hypersplenism due to Budd-Chiari syndrome (1), gastrointestinal bleeding (1) or the initial hemoglobin level was slightly below the level as provided by the criteria, but the level showed a rising pattern despite cytoreductive therapy (2).
1264464
 MALE Adult
Advisability of surgical treatment for chronic membranous obstruction of the hepatic portion of the inferior vena cava.
Jortner R, Shaklai M, Pinkhas J, Garty I, Levy M, de Vries A.
Pahlavi Med J. 1976;7(1):106-18.
Transatrial membranotomy was performed in a patient with membranous obstruction of the hepatic segment of the inferior vena cava, manifesting as longstanding varicosity and edema of the legs, chronic type of Budd-Chiari syndrome, liver cirrhosis and hypersplenism.