Budd-Chiari syndrome

Budd-Chiari syndrome (BCS) is caused by obstruction of hepatic venous outflow involving either the hepatic veins or the terminal segment of the inferior vena cava.

Lupus anticoagulant

Presence of lupus anticoagulant (LA) autoantibodies. LA represent a heterogeneous group of autoantibodies, IgG, IgM, or a mixture of both classes, that interfere with standard phospholipid-based coagulant tests (this is only an in vitro phenomenon, LA do not cause reduction of coagulation in vivo). The antibodies are directed against plasma proteins which also bind to phospholipid surfaces.


Total: 13

                       


(per page)
PMID (PMCID)
12924661
 FEMALE Adult
Suprahepatic Budd-Chiari syndrome treated with thrombectomy and cavoplasty.
Rhee J, Demetris AJ, Abu Elmagd K, Rabinovitz M.
Dig Dis Sci. 2003;48(8):1637-41.
The case of a 42-year-old female with Budd-Chiari syndrome (BCS) and lupus anticoagulant is reported.
10071347
 MIXED_SAMPLE Adult
Budd-Chiari syndrome associated with factor V leiden mutation: a report of 6 patients.
Hoffman R, Nimer A, Lanir N, Brenner B, Baruch Y.
Liver Transpl Surg. 1999;5(2):96-100.
We report 6 patients with Budd-Chiari syndrome associated with factor V Leiden mutation combined with another acquired thrombophilic state (myeloproliferative disorder and lupus anticoagulant in 3 cases) and without another thrombophilic disorder in the other 3 cases.
8063206
 FEMALE Adult
Budd-Chiari syndrome in a young patient with anticardiolipin antibodies: need for prolonged anticoagulant treatment.
Ouwendijk RJ, Koster JC, Wilson JH, Stibbe J, Lameris JS, Visser W, Benhamou JP.
Gut. 1994;35(7):1004-6.
The case of a 20 year old woman is reported with Budd-Chiari syndrome in whom lupus anticoagulant and anticardiolipin antibodies were shown; treatment with oral anticoagulants induced a considerable improvement.
8063206
 FEMALE Adult
Budd-Chiari syndrome in a young patient with anticardiolipin antibodies: need for prolonged anticoagulant treatment.
Ouwendijk RJ, Koster JC, Wilson JH, Stibbe J, Lameris JS, Visser W, Benhamou JP.
Gut. 1994;35(7):1004-6.
In conclusion patients with Budd-Chiari syndrome should be tested for lupus anticoagulants and anticardiolipin antibodies, Budd-Chiari syndrome resulting from this cause may have a good response to treatment with oral anticoagulants; this treatment should be maintained permanently, and pregnancy in such patients may initiate serious difficulties.
8063206
 FEMALE Adult
Budd-Chiari syndrome in a young patient with anticardiolipin antibodies: need for prolonged anticoagulant treatment.
Ouwendijk RJ, Koster JC, Wilson JH, Stibbe J, Lameris JS, Visser W, Benhamou JP.
Gut. 1994;35(7):1004-6.
In conclusion patients with Budd-Chiari syndrome should be tested for lupus anticoagulants and anticardiolipin antibodies, Budd-Chiari syndrome resulting from this cause may have a good response to treatment with oral anticoagulants; this treatment should be maintained permanently, and pregnancy in such patients may initiate serious difficulties.
1747329
 MALE Adult
Association of the Budd-Chiari syndrome with lupus anticoagulant. Case report and critical review.
Bisbocci D, De Micheli AG, Tamanti P, Cantoni R, Pellacani A, Pinna G, Marinone C, Chiandussi L.
Ann Ital Med Int. 1991;6(2):251-5.
Association of the Budd-Chiari syndrome with lupus anticoagulant.
2152314
 FEMALE Adult
[Budd-Chiari syndrome, pulmonary thromboembolism, and deep venous thrombosis associated with "lupus anticoagulant" and recent use of oral contraceptives].
Bacci S, Urquiola G, del Medico P, Sanabria JA, Bacci JC, Guzman M, Poleo JR.
G E N. 1990;44(3):237-42.
[Budd-Chiari syndrome, pulmonary thromboembolism, and deep venous thrombosis associated with "lupus anticoagulant" and recent use of oral contraceptives].
3091680
 MIXED_SAMPLE Adult
'Lupus' anticoagulant and thrombosis of the hepatic veins (Budd-Chiari syndrome). Report of three patients and review of the literature.
Van Steenbergen W, Beyls J, Vermylen J, Fevery J, Marchal G, Desmet V, De Groote J.
J Hepatol. 1986;3(1):87-94.
An active search for the 'lupus' anticoagulant should be performed to lower the percentage of apparently idiopathic cases of Budd-Chiari syndrome.
3087300
 FEMALE Adult
Budd-Chiari syndrome as the major thrombotic complication of systemic lupus erythematosus with the lupus anticoagulant.
Averbuch M, Levo Y.
Ann Rheum Dis. 1986;45(5):435-7.
We believe that the Budd-Chiari syndrome was part of her tendency for thrombosis, induced by the presence of a lupus anticoagulant.
3086175
 FEMALE Adult
Transformation of inferior vena caval thrombosis to membranous obstruction in a patient with the lupus anticoagulant.
Terabayashi H, Okuda K, Nomura F, Ohnishi K, Wong P.
Gastroenterology. 1986;91(1):219-24.
She was found to have circulating lupus anticoagulant that could have been causally related to the thrombosis and hence the Budd-Chiari syndrome.
6416918
 MALE Adult
Budd-Chiari syndrome in a patient with the lupus anticoagulant.
Pomeroy C, Knodell RG, Swaim WR, Arneson P, Mahowald ML.
Gastroenterology. 1984;86(1):158-61.
Budd-Chiari syndrome in a patient with the lupus anticoagulant.
6416918
 MALE Adult
Budd-Chiari syndrome in a patient with the lupus anticoagulant.
Pomeroy C, Knodell RG, Swaim WR, Arneson P, Mahowald ML.
Gastroenterology. 1984;86(1):158-61.
This report describes the first case of Budd-Chiari syndrome associated with the lupus anticoagulant.
6416918
 MALE Adult
Budd-Chiari syndrome in a patient with the lupus anticoagulant.
Pomeroy C, Knodell RG, Swaim WR, Arneson P, Mahowald ML.
Gastroenterology. 1984;86(1):158-61.
No medical condition known to predispose to an increased thrombotic tendency could be identified, and the presence of the lupus anticoagulant in the patient's plasma may provide an explanation for his hypercoagulability and development of the Budd-Chiari syndrome.