Budd-Chiari syndrome

Budd-Chiari syndrome (BCS) is caused by obstruction of hepatic venous outflow involving either the hepatic veins or the terminal segment of the inferior vena cava.

Portal vein thrombosis

Thrombosis of the portal vein and/or its tributaries, which include the splenic vein and the sup-erior and inferior mesenteric veins.


Total: 19

                       


(per page)
PMID (PMCID)
28483616
 MALE Middle Aged
Endovascular Treatment of an Unusual Membranous Obstruction of the Inferior Vena Cava in Budd-Chiari Syndrome Complicated by Mural Portal Vein Thrombosis.
Zhang WG, Liu DM, Han XW, Ren JZ, Zhou PL, Wang ZG.
Ann Vasc Surg. 2017;44:419.e13-419.e17.
Endovascular Treatment of an Unusual Membranous Obstruction of the Inferior Vena Cava in Budd-Chiari Syndrome Complicated by Mural Portal Vein Thrombosis.
28483616
 MALE Middle Aged
Endovascular Treatment of an Unusual Membranous Obstruction of the Inferior Vena Cava in Budd-Chiari Syndrome Complicated by Mural Portal Vein Thrombosis.
Zhang WG, Liu DM, Han XW, Ren JZ, Zhou PL, Wang ZG.
Ann Vasc Surg. 2017;44:419.e13-419.e17.
We describe the case of a patient with Budd-Chiari syndrome who presented with an unusual membranous obstruction of the inferior vena cava complicated by massive portal vein thrombosis (PVT).
30363345
(6159308)
 OTHER
Rescue from liver transplantation: TIPSS and thrombectomy successfully treat a case of acute Budd-Chiari syndrome complicated by portal vein thrombosis.
Townsend SA, Karkhanis S, Tripathi D, Mueisan P, Zia Z, Elsharkawy AM.
BJR Case Rep. 2017;3(1):20160059.
This is a rare case report of a patient meeting liver transplant criteria secondary to acute Budd-Chiari syndrome and complete portal vein thrombosis, which was managed successfully entirely by radiological means; this technique could be used to avoid or act as a bridge to liver transplantation in the future.
30363345
(6159308)
 OTHER
Rescue from liver transplantation: TIPSS and thrombectomy successfully treat a case of acute Budd-Chiari syndrome complicated by portal vein thrombosis.
Townsend SA, Karkhanis S, Tripathi D, Mueisan P, Zia Z, Elsharkawy AM.
BJR Case Rep. 2017;3(1):20160059.
We report the rare case of a female who presented with fulminant liver failure secondary to acute Budd-Chiari syndrome and complete portal vein thrombosis.
30363345
(6159308)
 OTHER
Rescue from liver transplantation: TIPSS and thrombectomy successfully treat a case of acute Budd-Chiari syndrome complicated by portal vein thrombosis.
Townsend SA, Karkhanis S, Tripathi D, Mueisan P, Zia Z, Elsharkawy AM.
BJR Case Rep. 2017;3(1):20160059.
Rescue from liver transplantation: TIPSS and thrombectomy successfully treat a case of acute Budd-Chiari syndrome complicated by portal vein thrombosis.
25121018
 OTHER
Multiple abdominal veins thrombosis secondary to protein s deficiency - a case report.
Kodali VU, Borra S, Mandarapu SB, Sanda MR, Bolla SR.
J Clin Diagn Res. 2014;8(6):MD07-8.
Abdominal venous thrombosis may present either as Budd-Chiari syndrome (BCS) caused by hepatic vein or proximal inferior vena cava (IVC) obstruction or as an extra hepatic portal obstruction (EHPVO) caused by Portal vein thrombosis or mesenteric vein thrombosis, but a mixed involvement is uncommon.
23277116
 FEMALE Middle Aged
Successful liver transplantation in a patient with splanchnic vein thrombosis and pulmonary embolism due to polycythemia vera with Jak2v617f mutation and heparin-induced thrombocytopenia.
Biagioni E, Pedrazzi P, Marietta M, Di Benedetto F, Villa E, Luppi M, Girardis M.
J Thromb Thrombolysis. 2013;36(3):352-4.
We report the first case of successful urgent liver transplantation (LT) in a patient with end-stage liver disease due to a Budd-Chiari syndrome, portal vein thrombosis and pulmonary embolism due to acquired thrombophilia associated to polycythemia vera carrying JAK2V617F gene mutation and HIT in the acute phase.
21505581
(3056429)
 MALE Adult
Splanchnic vein thrombosis, the onset manifestation in JAK positive Chronic Myeloproliferative Disorders Neoplasms.
Vladareanu AM, Popov V, Bumbea H, Onisai M, Ilea A, Dobrea C, Miulescu M.
J Med Life. 2011;4(1):97-101.
We present three patients with portal vein thrombosis and Budd Chiari syndrome, who were further diagnosed with MPN-the thrombosis was the onset event of the disease.
17969202
 FEMALE Adult
Use of splenic artery embolization to relieve tense ascites following liver transplantation in a patient with paroxysmal nocturnal hemoglobinuria.
Chang CY, Singal AK, Ganeshan SV, Schiano TD, Lookstein R, Emre S.
Liver Transpl. 2007;13(11):1532-7.
We describe a patient who developed refractory ascites due to portal vein thrombosis following liver transplantation for Budd-Chiari syndrome in the setting of paroxysmal nocturnal hemoglobinuria.
16529659
(1421416)
 FEMALE Adult
Acute partial Budd-Chiari syndrome and portal vein thrombosis in cytomegalovirus primary infection: a case report.
Spahr L, Cerny A, Morard I, Rubbia-Brandt L, Schrenzel J.
BMC Gastroenterol. 2006;6:10.
Acute partial Budd-Chiari syndrome and portal vein thrombosis in cytomegalovirus primary infection: a case report.
16504889
 FEMALE Adult
Budd-Chiari syndrome and acute portal vein thrombosis: management by a transjugular intrahepatic portosystemic shunt (TIPS) and portal vein interventions via a TIPS.
Kori I, Bar-Zohar D, Carmiel-Haggai M, Samuels D, Nakache R, Oren R, Kessler A, Szold O, Ben-Haim M.
J Gastrointest Surg. 2006;10(3):417-21.
Budd-Chiari syndrome and acute portal vein thrombosis: management by a transjugular intrahepatic portosystemic shunt (TIPS) and portal vein interventions via a TIPS.
15223461
 MALE Middle Aged
Budd-Chiari syndrome and portal vein thrombosis due to right atrial myxoma.
Anagnostopoulos GK, Margantinis G, Kostopoulos P, Papadopoulou G, Roulias A, Sakorafas G, Liassis N.
Ann Thorac Surg. 2004;78(1):333-4.
Budd-Chiari syndrome and portal vein thrombosis due to right atrial myxoma.
12772054
 FEMALE Adult
The transjugular intrahepatic portosystemic stent-shunt (TIPS) as rescue therapy for complete Budd-Chiari syndrome and portal vein thrombosis.
Opitz T, Buchwald AB, Lorf T, Awuah D, Ramadori G, Nolte W.
Z Gastroenterol. 2003;41(5):413-8.
In the present case TIPS simultaneously allowed the diagnosis of portal vein thrombosis and served as rescue therapy of complicated Budd-Chiari syndrome.
12111088
 FEMALE Middle Aged
Primary antiphospholipid syndrome presenting with abdominal angina and splenic infarction.
Choi BG, Jeon HS, Lee SO, Yoo WH, Lee ST, Ahn DS.
Rheumatol Int. 2002;22(3):119-21.
Gastrointestinal manifestations associated with vascular occlusion include Budd-Chiari syndrome, hepatic and splenic infarction, pancreatitis, omental and intestinal infarction, and esophageal variceal bleeding due to portal vein thrombosis, but chronic mesenteric ischemia associated with mesenteric arterial thrombosis is very rare in this syndrome.
10901722
 FEMALE Middle Aged
Erythematous plaques due to platelet plugging: a clue to underlying myeloproliferative disorder.
Stone MS, Robson KJ, Piette WW.
J Am Acad Dermatol. 2000;43(2 Pt 2):355-7.
These cutaneous findings occurred in association with progressive inferior vena cava and portal vein thrombosis while on coumarin anticoagulation, following hepatic transplantation for Budd-Chiari syndrome.
9072481
 FEMALE Adult
[TIPSS in the Budd-Chiari syndrome with portal vein thrombosis].
Nolte W, Figulla HR, Ringe B, Wiltfang J, Munke H, Hartmann H, Ramadori G.
Dtsch Med Wochenschr. 1997;122(5):116-21.
[TIPSS in the Budd-Chiari syndrome with portal vein thrombosis].
9072481
 FEMALE Adult
[TIPSS in the Budd-Chiari syndrome with portal vein thrombosis].
Nolte W, Figulla HR, Ringe B, Wiltfang J, Munke H, Hartmann H, Ramadori G.
Dtsch Med Wochenschr. 1997;122(5):116-21.
This case demonstrates the effectiveness of TIPSS in Budd-Chiari syndrome, even in complicated portal vein thrombosis.
8464558
 MALE Adult
[The Senning procedure in Budd-Chiari syndrome associated with complete portal vein thrombosis].
Belghiti J, Di Carlo I, Sauvanet A, Fekete F.
Minerva Chir. 1993;48(1-2):65-71.
[The Senning procedure in Budd-Chiari syndrome associated with complete portal vein thrombosis].
1257853
 MALE Adult
Portal vein thrombosis with ascites. A case report.
Penek J, Webber BL, Kirsch RE.
S Afr Med J. 1976;50(6):173-6.
The experience at Groote Schuur Hospital of portal vein thrombosis and Budd-Chiari syndrome between 1964 and 1974 is summarised and the literature is reviewed.