Budd-Chiari syndrome

Budd-Chiari syndrome (BCS) is caused by obstruction of hepatic venous outflow involving either the hepatic veins or the terminal segment of the inferior vena cava.

Hepatic vein thrombosis

An obstruction in the veins of the liver caused by a blood clot (thrombosis).


Total: 31

                       


(per page)
PMID (PMCID)
29381999
(5708998)
 FEMALE Middle Aged
Abdominal surgery in patients with essential thrombocythemia: A case report and systematic review of literature.
Zhu Y, Jiang H, Chen Z, Lu B, Wu J.
Medicine (Baltimore). 2017;96(47):e8856.
There was one case of pseudohyperkalemia after surgery and one case of Budd-Chiari syndrome caused by hepatic vein thrombosis.
28355402
 FEMALE Adult
Budd-Chiari syndrome secondary to catheter-associated inferior vena cava thrombosis.
Araujo GN, Restelatto LM, Prompt CA, Karohl C.
J Bras Nefrol. 2017;39(1):91-94.
Budd-Chiari syndrome is a rare medical condition caused by hepatic veins thrombosis.
26361700
 MALE Young Adult
Liver Transplantation for Budd-Chiari Syndrome With Large Solitary Focal Nodular Hyperplasia of the Liver in a Patient With Essential Thrombocythemia: Case Report. [Corrected].
Alnajjar A, Al-Hussaini H, Al Sebayel M, Al-Kattan W, Elsiesy H.
Transplant Proc. 2015;47(7):2282-6.
Imaging revealed hepatic vein thrombosis, confirming Budd-Chiari syndrome, and a 6.2 6.1 6.8cm lesion in segment 8 of the liver.
23210433
(3514094)
 OTHER
Eculizumab in paroxysmal nocturnal hemoglobinuria with Budd-Chiari syndrome progressing despite anticoagulation.
Brodsky A, Mazzocchi O, Sanchez F, Khursigara G, Malhotra S, Volpacchio M.
Exp Hematol Oncol. 2012;1(1):26.
Hepatic vein thrombosis (Budd-Chiari syndrome) is common in PNH patients.
20455413
 FEMALE Adult
[Cyclospora cayetanensis and Cryptosporidium parvum coinfection in a pregnant woman with prolonged diarrhoea].
Dogan N, Saglik I.
Mikrobiyol Bul. 2010;44(1):155-9.
However, hepatic vein thrombosis and liver failure have developed in the postnatal period and she was diagnosed as Budd-Chiari syndrome.
19117529
(2648948)
 OTHER
Stent angioplasty of narrowed portocaval shunt in Budd Chiari syndrome: a case report.
Doctor N, Gandhi V, Shah S, Hussain M, Marar S, Philip S.
Cases J. 2009;2(1):1.
Hepatic vein thrombosis (Budd-Chiari Syndrome) is a rare disorder resulting from an obstruction to the outflow of blood from the liver.
16517788
 MIXED_SAMPLE Adult
Catheter-directed thrombolysis and thrombectomy for the Budd-Chiari syndrome in paroxysmal nocturnal hemoglobinuria in three patients.
Kuo GP, Brodsky RA, Kim HS.
J Vasc Interv Radiol. 2006;17(2 Pt 1):383-7.
Patients with hepatic vein thrombosis (Budd-Chiari syndrome) can present with abdominal pain, hepatomegaly, jaundice, and ascites.
16827884
 MIXED_SAMPLE Adult
Elevated serum erythropoietin levels in patients with Budd-Chiari syndrome secondary to polycythemia vera: clinical implications for the role of JAK2 mutation analysis.
Thurmes PJ, Steensma DP.
Eur J Haematol. 2006;77(1):57-60.
The purpose of this study was to use JAK2 V617F analysis to re-evaluate the validity of elevated Epo levels as a PV-exclusion criterion in patients with hepatic vein thrombosis [Budd-Chiari syndrome (BCS)].
16607082
 MALE Adult
Hepatic vein thrombosis leading to fulminant hepatic failure in a case of acute non-promyelocytic myelogenous leukemia.
Amitrano L, Guardascione MA, Schiavone EM, Brancaccio V, Antinolfi I, Iannaccone L, Ferrara F, Balzano A.
Blood Coagul Fibrinolysis. 2006;17(1):59-61.
Common causes of Budd-Chiari syndrome are chronic myeloproliferative disorders, while acute leukemia has been associated with hepatic vein thrombosis in only two cases in the literature to date.
16247755
 FEMALE
Possible association between Budd-Chiari Syndrome and gemtuzumab ozogamicin treatment in a patient with refractory acute myelogenous leukemia.
Kurt M, Shorbagi A, Altundag K, Elkiran T, Gullu I, Kansu E.
Am J Hematol. 2005;80(3):213-5.
A patient who developed Budd-Chiari Syndrome with hepatic vein thrombosis following treatment with GO is presented.
16218798
 MIXED_SAMPLE Adult
Unusual thromboses associated with protein S deficiency in patients with acquired immunodeficiency syndrome: case reports and review of the literature.
Dillmon MS, Saag MS, Hamza SH, Adler BK, Marques MB.
AIDS Res Hum Retroviruses. 2005;21(9):753-6.
The second patient presented with hepatic vein thrombosis (Budd-Chiari syndrome) and was also PS deficient.
15243394
 MALE Adult
[Paroxysmal nocturnal hemoglobinuria revealed by hepatic vein thrombosis (Budd-Chiari syndrome) during Infliximab therapy].
Sobkeng Goufack E, Mammou S, Scotto B, De Muret A, Maakaroun A, Socie G, Bacq Y.
Gastroenterol Clin Biol. 2004;28(6-7 Pt 1):596-9.
[Paroxysmal nocturnal hemoglobinuria revealed by hepatic vein thrombosis (Budd-Chiari syndrome) during Infliximab therapy].
12243558
 FEMALE Adult
Coexistence of homozygous factor V Leiden mutation and antiphospholipid antibodies in two patients presented with Budd-Chiari syndrome.
Diz-Kucukkaya R, Demir K, Yenerel MN, Nalcaci M, Kaymakoglu S, Inanc M.
Haematologia (Budap). 2002;32(1):73-7.
Two female patients are reported, who presented with Budd-Chiari syndrome (hepatic vein thrombosis), and were found to have both, antiphospholipid antibodies and homozygous factor V Leiden mutation.
9332072
 FEMALE Middle Aged
[Budd-Chiari syndrome].
Goland S, Malnick SD, Shvidel L, Mor E, Sthoeger ZM, Evron E.
Harefuah. 1997;133(3-4):96-8, 167.
Budd Chiari syndrome is a rare disorder resulting from occlusion of hepatic venous drainage by hepatic vein thrombosis or by a membranous web in the inferior vena cava.
8968799
 FEMALE Adult
Budd-Chiari syndrome caused by hepatic vein thrombosis in a patient with myeloproliferative disorder.
Usui T, Kitano K, Midorikawa T, Yoshizawa K, Kobayashi H, Tanaka E, Matsunami H, Kawasaki S, Kiyosawa K.
Intern Med. 1996;35(11):871-5.
Budd-Chiari syndrome caused by hepatic vein thrombosis in a patient with myeloproliferative disorder.
7963425
 MIXED_SAMPLE Adult
Antiphospholipid syndrome as the second cause of non-tumorous Budd-Chiari syndrome.
Pelletier S, Landi B, Piette JC, Ekert P, Coutellier A, Desmoulins C, Fadlallah JP, Herson S, Valla D.
J Hepatol. 1994;21(1):76-80.
In a prospective study of 22 patients with non-tumorous Budd-Chiari syndrome, four were found to have the antiphospholipid syndrome with no other cause of hepatic vein thrombosis.
8309615
 MALE Middle Aged
[Subacute Budd-Chiari syndrome treated with rTPA. Considerations on a case].
Nardini A, Falco E, Celoria G, Neviani AL, Stefani R, Gadducci G, Astesana L, Spinetta G.
Minerva Chir. 1993;48(19):1129-33.
The authors report on a case of hepatic vein thrombosis or Budd-Chiari syndrome (BCS) successfully treated with recombinant Tissue Plasminogen Activator (rTPA).
2066958
 MIXED_SAMPLE Adult
Budd-Chiari syndrome in association with Behcet's disease.
al-Dalaan A, al-Balaa S, Ali MA, Huraib S, Amin T, al-Maziad A, al-Fadda M.
J Rheumatol. 1991;18(4):622-6.
Benign intracranial hypertension was the chief presenting complaint in one patient, who later suffered extensive inferior vena caval and hepatic vein thrombosis, with manifestations of Budd-Chiari syndrome.
2007158
 FEMALE Adult
Hepatic vein thrombosis in a teenager: a case report.
Barnet B, Joffe A.
J Adolesc Health. 1991;12(1):60-2.
Hepatic vein thrombosis or the Budd-Chiari syndrome is an uncommon condition which rarely occurs in teenagers.
2046772
 FEMALE Child
[Intestinal obstruction caused by non-absorbable tablets and Budd-Chiari syndrome in a patient with Crohn's disease].
Witteman BJ, Weterman IT, Griffioen G, Lamers CB.
Ned Tijdschr Geneeskd. 1991;135(17):766-9.
During an exacerbation of Crohn's disease she developed hepatic vein thrombosis with a Budd-Chiari syndrome (upper abdominal pain, hepatomegaly and ascites).