Cutis marmorata telangiectatica congenita

Cutis marmorata telangiectatica congenita (CMTC) is a congenital localized or generalized vascular anomaly characterized by a persistent cutis marmorata pattern with a marbled bluish to deep purple appearance, spider nevus-like telangiectasia, phlebectasia and, occasionally, ulceration and atrophy of the affected skin.

Pulmonary lymphangiectasia

Abnormal dilatation of the pulmonary lymphatic vessels. Lymphatic fluid in the lung is derived from normal leakage of fluid out of the blood capillaries in the lung. In pulmonary lymphangiectasia, the pulmonary lymphatics are not properly connected and become dilated with fluid.


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(per page)
PMID (PMCID)
29791897
OTHER
Cutis Marmorata Telangiectatica Congenita Presenting as a Fetal Hemothorax.
Mon RA, Mozurkewich E, Treadwell MC, Berman DR.
Fetal Diagn Ther. 2019;45(4):281-284.
Postnatal workup established the diagnoses of cutis marmorata telangiectatica congenita (CMTC) and pulmonary lymphangiectasia.