Hemophagocytic syndrome associated with an infection


Immunodeficiency

Failure of the immune system to protect the body adequately from infection, due to the absence or insufficiency of some component process or substance.


Total: 2

                       


(per page)
PMID (PMCID)
10814994
 MALE Infant
Large deletion of the X-linked lymphoproliferative disease gene detected by fluorescence in situ hybridization.
Honda K, Kanegane H, Eguchi M, Kimura H, Morishima T, Masaki K, Tosato G, Miyawaki T, Ishii E.
Am J Hematol. 2000;64(2):128-32.
The X-linked lymphoproliferative disease (XLP) is an inherited immunodeficiency characterized by an abnormal responses to infection with Epstein-Barr virus (EBV), resulting in fatal infectious mononucleosis, hypogammaglobulinemia, virus-associated hemophagocytic syndrome, and malignant lymphoma.
3307293
 MIXED_SAMPLE Infant
Immunohistochemical and ultrastructural studies on histiocytosis in children.
Wakuya J.
Acta Pathol Jpn. 1987;37(6):901-13.
Thirty-four cases of eosinophilic granulomas, 18 cases of diffuse histiocytosis-X, 2 cases of Letterer-Siwe-like syndrome with immunodeficiency, 4 cases of malignant histiocytosis and virus associated hemophagocytic syndrome were studied.