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Diencephalic syndrome

Diencephalic syndrome (DS) is a rare condition characterized by profound emaciation and failure to thrive (with normal caloric intake and normal linear growth), hyperalertness, hyperkinesia and euphoria, in the presence of hypothalamic tumors.

Neoplasm

An organ or organ-system abnormality that consists of uncontrolled autonomous cell-proliferation which can occur in any part of the body as a benign or malignant neoplasm (tumour).

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PMID (PMCID)
27872228	FEMALE	Infant
	Child Neurology: Diencephalic syndrome-like presentation of a cervicomedullary brainstem tumor.
	Conway M, Ejaz R, Kouzmitcheva E, Savlov D, Rutka JT, Moharir M. Neurology. 2016;87(21):e248-e251.
	Diencephalic syndrome is a rare clinical entity, traditionally encompassing severe failure to thrive, nystagmus, and hyperkinesis, secondary to an intracranial neoplasm that is classically located in the hypothalamic region and its vicinity.