Inflammatory myofibroblastic tumor

Inflammatory myofibroblastic tumor is a rare neoplastic lesion of the submucosal stroma, which can develop in any organ, often occurring in the lung, mesentery, omentum and the retroperitoneal region. It is histologically heterogenous, composed of spindle-shaped cells, myofibroblasts and inflammatory cells. It is usually benign, however local invasion, recurrence, malignant transformation with vascular invasion and metastases may occur. The presentation is nonspecific and depends on the organ involved. Some patients may present with paraneoplastic syndrome (fever, malaise, weight loss, anemia, thrombocytosis) or symptoms related to compression of adjacent organs, such as bowel obstruction.

Cyanosis

Bluish discoloration of the skin and mucosa due to poor circulation or inadequate oxygenation of arterial or capillary blood.


Total: 2

                      


(per page)
PMID (PMCID)
23280044
FEMALE Infant
An unexpected cause of respiratory distress and cyanosis: cardiac inflammatory myofibroblastic tumor.
Elkiran O, Karakurt C, Erdil N, Disli OM, Dagli AF.
Congenit Heart Dis. 2013;8(6):E174-7.
We report a rare case of inflammatory myofibroblastic tumors of the right ventricle in a 7-month-old girl presenting with respiratory distress and cyanosis.
23280044
FEMALE Infant
An unexpected cause of respiratory distress and cyanosis: cardiac inflammatory myofibroblastic tumor.
Elkiran O, Karakurt C, Erdil N, Disli OM, Dagli AF.
Congenit Heart Dis. 2013;8(6):E174-7.
An unexpected cause of respiratory distress and cyanosis: cardiac inflammatory myofibroblastic tumor.