Evans syndrome

A rare chronic hematologic disorder characterized by the simultaneous or sequential association of autoimmune hemolytic anemia (AIHA; a disorder in which auto-antibodies are directed against red blood cells causing anemia of varying degrees of severity) with immune thrombocytopenic purpura (ITP; a coagulation disorder in which auto-antibodies are directed against platelets causing hemorrhagic episodes) and occasionally autoimmune neutropenia, in the absence of a known underlying etiology.

Edema

An abnormal accumulation of fluid beneath the skin, or in one or more cavities of the body.

Total: 2

(per page)

PMID (PMCID)
22030016	FEMALE	Middle Aged
	Dermatomyositis associated with generalized subcutaneous edema and Evans syndrome.
	Jung KD, Kim PS, Park HY, Kim CR, Byun JY, Lee DY, Lee JH, Yang JM, Lee ES. J Am Acad Dermatol. 2012;66(1):144-7.
	Treatment with high-dose glucocorticoids and an immunosuppressive agent controlled the DM, the generalized subcutaneous edema, and the Evans syndrome.
22030016	FEMALE	Middle Aged
	Dermatomyositis associated with generalized subcutaneous edema and Evans syndrome.
	Jung KD, Kim PS, Park HY, Kim CR, Byun JY, Lee DY, Lee JH, Yang JM, Lee ES. J Am Acad Dermatol. 2012;66(1):144-7.
	We report the case of a 52-year-old Korean woman who presented with generalized subcutaneous edema, an erythematous rash, dysphagia, and proximal muscle weakness, and subsequently developed features of Evans syndrome.