Evans syndrome

A rare chronic hematologic disorder characterized by the simultaneous or sequential association of autoimmune hemolytic anemia (AIHA; a disorder in which auto-antibodies are directed against red blood cells causing anemia of varying degrees of severity) with immune thrombocytopenic purpura (ITP; a coagulation disorder in which auto-antibodies are directed against platelets causing hemorrhagic episodes) and occasionally autoimmune neutropenia, in the absence of a known underlying etiology.

Vitiligo



Total: 1

                      


(per page)
PMID (PMCID)
2304424
FEMALE Adult
Systemic Castleman's disease in association with Evan's syndrome and vitiligo.
Marsh JH, Colbourn DS, Donovan V, Staszewski H.
Med Pediatr Oncol. 1990;18(2):169-72.
We report a case of the plasma cell variant of Castleman's disease that was associated with autoimmune hemolytic anemia and autoimmune thrombocytopenia (Evan's syndrome), and vitiligo, the association of which has not been previously reported.