Evans syndrome

A rare chronic hematologic disorder characterized by the simultaneous or sequential association of autoimmune hemolytic anemia (AIHA; a disorder in which auto-antibodies are directed against red blood cells causing anemia of varying degrees of severity) with immune thrombocytopenic purpura (ITP; a coagulation disorder in which auto-antibodies are directed against platelets causing hemorrhagic episodes) and occasionally autoimmune neutropenia, in the absence of a known underlying etiology.

Pancytopenia

An abnormal reduction in numbers of all blood cell types (red blood cells, white blood cells, and platelets).

Total: 2

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PMID (PMCID)
11786723	MALE
	Bronchiolitis obliterans organizing pneumonia associated with Evans syndrome.
	Maiz L, Munoz A, Maldonado S, Pacheco A, Lamas A, Fogue L. Respiration. 2001;68(6):631-4.
	The association of bronchiolitis obliterans organizing pneumonia (BOOP) with insulin-dependent diabetes mellitus (IDDM) and Evans syndrome (autoimmune pancytopenia) has not been reported previously.
9081810	FEMALE	Adult
	[Immune thrombocytopenia, anemia and leukopenia during pregnancy. Successful therapy with extracorporeal immunoadsorption].
	Julius U, Patzak A, Schaich M, Ehninger G, Kamin G. Dtsch Med Wochenschr. 1997;122(8):220-4.
	The pancytopenia with immune thrombocytopenia, autohaemolytic anaemia and associated leukopenia were classified as Evans syndrome.