Evans syndrome

A rare chronic hematologic disorder characterized by the simultaneous or sequential association of autoimmune hemolytic anemia (AIHA; a disorder in which auto-antibodies are directed against red blood cells causing anemia of varying degrees of severity) with immune thrombocytopenic purpura (ITP; a coagulation disorder in which auto-antibodies are directed against platelets causing hemorrhagic episodes) and occasionally autoimmune neutropenia, in the absence of a known underlying etiology.

Reticulocytopenia

A reduced number of reticulocytes in the peripheral blood.


Total: 1

                      


(per page)
PMID (PMCID)
29531655
(5841940)
OTHER
Parvovirus B19-triggered Acute Hemolytic Anemia and Thrombocytopenia in a Child with Evans Syndrome.
Zikidou P, Grapsa A, Bezirgiannidou Z, Chatzimichael A, Mantadakis E.
Mediterr J Hematol Infect Dis. 2018;10(1):e2018018.
We describe a 14-year-old girl with long-standing Evans syndrome, who presented with severe anemia, reticulocytopenia and thrombocytopenia.