Evans syndrome

A rare chronic hematologic disorder characterized by the simultaneous or sequential association of autoimmune hemolytic anemia (AIHA; a disorder in which auto-antibodies are directed against red blood cells causing anemia of varying degrees of severity) with immune thrombocytopenic purpura (ITP; a coagulation disorder in which auto-antibodies are directed against platelets causing hemorrhagic episodes) and occasionally autoimmune neutropenia, in the absence of a known underlying etiology.

Myelofibrosis

Replacement of bone marrow by fibrous tissue.

Total: 3

(per page)

PMID (PMCID)
28584963	FEMALE	Middle Aged
	Steroid-resistant autoimmune myelofibrosis in a patient with autoimmune hepatitis and Evans syndrome complicated with increased expression of TGF-beta in the bone marrow: a case report.
	Ohkawara H, Furukawa M, Ikeda K, Shichishima-Nakamura A, Fukatsu M, Sano T, Ueda K, Kimura S, Kanai R, Oka Y, Murakami F, Suzuki O, Hashimoto Y, Ogawa K, Ikezoe T. Int J Hematol. 2017;106(5):718-724.
	Steroid-resistant autoimmune myelofibrosis in a patient with autoimmune hepatitis and Evans syndrome complicated with increased expression of TGF-946 in the bone marrow: a case report.
8532392	FEMALE
	Evans' syndrome, myelofibrosis and systemic lupus erythematosus: role of procollagens in myelofibrosis.
	Ramakrishna R, Kyle PW, Day PJ, Manoharan A. Pathology. 1995;27(3):255-9.
	We describe an 18 yr old female with systemic lupus erythematosus presenting with Evans' syndrome (autoimmune hemolytic anemia and immune thrombocytopenia) and dense myelofibrosis.
8532392	FEMALE
	Evans' syndrome, myelofibrosis and systemic lupus erythematosus: role of procollagens in myelofibrosis.
	Ramakrishna R, Kyle PW, Day PJ, Manoharan A. Pathology. 1995;27(3):255-9.
	Evans' syndrome, myelofibrosis and systemic lupus erythematosus: role of procollagens in myelofibrosis.