Endocardial fibroelastosis

Endomyocardial fibroelastosis is a cause of unexplained childhood cardiac insufficiency. It results from diffuse thickening of the endocardium leading to dilated myocardiopathy in the majority of cases and restrictive myocardiopathy in rare cases. It may occur as a primary disorder or may be secondary to another cardiac malformation, notably aortic stenosis or atresia.

Hypertension

The presence of chronic increased pressure in the systemic arterial system.


Total: 4

                       


(per page)
PMID (PMCID)
24826287
(4008507)
 OTHER
Heart Transplantation in a 14-Year-Old Boy in the Presence of Severe Out-of-Proportion Pulmonary Hypertension due to Restrictive Left Heart Disease: A Case Report.
Schwienbacher M, Schweigmann U, Neu N, Schermer E, Velik-Salchner C, Michel-Behnke I, Irnberger E, Steger CM, Stein JI, Geiger R.
Case Rep Cardiol. 2013;2013:418565.
A 14-year-old boy after balloon valvuloplasty of severe aortic valve stenosis in the neonatal period was referred for heart-lung transplantation because of high grade pulmonary hypertension and left heart dysfunction due to endocardial fibroelastosis with severe mitral insufficiency.
9688767
 FEMALE Infant
Endocardial fibroelastosis in L-transposition of the great arteries with Ebstein's anomaly: revisited.
Dahdah NS, van Doesburg NH, Russo P.
Pediatr Dev Pathol. 1998;1(5):427-32.
We report here the case of an infant with a diagnosis of corrected transposition of the great arteries and Ebstein's deformity of the left-sided tricuspid valve who developed pulmonary hypertension and endocardial fibroelastosis, two unusual associations with this lesion.
8540931
 FEMALE Adult
Endocardial fibroelastosis: an unusual cause of pulmonary hypertension in pregnancy.
Mandel RI, Bruner JP.
Am J Perinatol. 1995;12(5):319-21.
A 23-year-old Caucasian primigravida with a history of congenital endocardial fibroelastosis and severe pulmonary hypertension presented at 20 weeks' gestation.
8540931
 FEMALE Adult
Endocardial fibroelastosis: an unusual cause of pulmonary hypertension in pregnancy.
Mandel RI, Bruner JP.
Am J Perinatol. 1995;12(5):319-21.
Endocardial fibroelastosis: an unusual cause of pulmonary hypertension in pregnancy.