Endocardial fibroelastosis

Endomyocardial fibroelastosis is a cause of unexplained childhood cardiac insufficiency. It results from diffuse thickening of the endocardium leading to dilated myocardiopathy in the majority of cases and restrictive myocardiopathy in rare cases. It may occur as a primary disorder or may be secondary to another cardiac malformation, notably aortic stenosis or atresia.

Congestive heart failure

The presence of an abnormality of cardiac function that is responsible for the failure of the heart to pump blood at a rate that is commensurate with the needs of the tissues or a state in which abnormally elevated filling pressures are required for the heart to do so. Heart failure is frequently related to a defect in myocardial contraction.


Total: 3

                      


(per page)
PMID (PMCID)
11704210
FEMALE
Doppler fetal echocardiography in endocardial fibroelastosis.
Weiner Z, Shalev E.
Obstet Gynecol. 2001;98(5 Pt 2):933-5.
Endocardial fibroelastosis is a congenital heart disease known to cause congestive heart failure in early infancy.
6464971
MIXED_SAMPLE Child
Anomalous origin of the left anterior descending coronary artery from the pulmonary artery.
Tamer DF, Mallon SM, Garcia OL, Wolff GS.
Am Heart J. 1984;108(2):341-5.
Two had had congestive heart failure in infancy with clinical diagnosis of endocardial fibroelastosis and all had abnormal ECGs.
501933
MALE Child
Cross-sectional echocardiographic findings of left ventricular thrombi in a ten-year-old patient with cardiomyopathy.
Suzuki S, Yanagisawa M, Yano S, Itoh K, Kotohda K.
Jpn Heart J. 1979;20(5):675-9.
Using cross-sectional echocardiography, left ventricular thrombi were easily found in a 10-year-old boy suffering from congestive heart failure resulting from long-standing endocardial fibroelastosis.