Endocardial fibroelastosis

Endomyocardial fibroelastosis is a cause of unexplained childhood cardiac insufficiency. It results from diffuse thickening of the endocardium leading to dilated myocardiopathy in the majority of cases and restrictive myocardiopathy in rare cases. It may occur as a primary disorder or may be secondary to another cardiac malformation, notably aortic stenosis or atresia.

Left ventricular hypertrophy

Enlargement or increased size of the heart left ventricle.


合計: 1

                      


(表示件数)
PMID (PMCID)
9185226
FEMALE
Autopsy findings in the Wolcott-Rallison syndrome.
Thornton CM, Carson DJ, Stewart FJ.
Pediatr Pathol Lab Med. 1997;17(3):487-96.
The heart was enlarged with mitral value dysplasia and stenosis, left atrial dilatation, left ventricular hypertrophy, and endocardial fibroelastosis.