Endocardial fibroelastosis

Endomyocardial fibroelastosis is a cause of unexplained childhood cardiac insufficiency. It results from diffuse thickening of the endocardium leading to dilated myocardiopathy in the majority of cases and restrictive myocardiopathy in rare cases. It may occur as a primary disorder or may be secondary to another cardiac malformation, notably aortic stenosis or atresia.

Atrial fibrillation

An atrial arrhythmia characterized by disorganized atrial activity without discrete P waves on the surface EKG, but instead by an undulating baseline or more sharply circumscribed atrial deflections of varying amplitude an frequency ranging from 350 to 600 per minute.


合計: 2

                      


(表示件数)
PMID (PMCID)
31182935
OTHER
An illustrative case of endocardial fibroelastosis and recalcitrant intracardiac thrombosis: a case report.
Ozdemir D, Cortopassi IO, McNamara RL.
Thromb J. 2019;17:8.
Herein, we describe a relatively asymptomatic patient with endocardial fibroelastosis who has been found to have atrial fibrillation and a large thrombus in the right atrium.
17926085
MALE Infant, Newborn
Neonatal atrial fibrillation after surgical repair of tracheoesophageal fistula with esophageal atresia.
Mainzer G, Khoury A, Gelernter-Yaniv L, Lorber A.
Pediatr Cardiol. 2008;29(1):150-2.
A report of 35 pediatric patients in a single center over a period of 22 years identified atrial fibrillation in children with a variety of ailments including congenital cardiac anomalies before and after corrective surgery, rheumatic valve disease, Marfan's syndrome with mitral regurgitation, infective endocarditis, cardiomyopathy, endocardial fibroelastosis, paroxysmal atrial tachycardia of infants, and cardiac tumors [2].