Endocardial fibroelastosis

Endomyocardial fibroelastosis is a cause of unexplained childhood cardiac insufficiency. It results from diffuse thickening of the endocardium leading to dilated myocardiopathy in the majority of cases and restrictive myocardiopathy in rare cases. It may occur as a primary disorder or may be secondary to another cardiac malformation, notably aortic stenosis or atresia.

Heart block

Impaired conduction of cardiac impulse occurring anywhere along the conduction pathway.

Total: 3

(per page)

PMID (PMCID)
22089457	FEMALE	Child
	Persistent fetal sinus bradycardia associated with maternal anti-SSA/Ro and anti-SSB/La antibodies.
	Chockalingam P, Jaeggi ET, Rammeloo LA, Haak MC, Adama van Scheltema PN, Breur JM, Bartelings MM, Clur SA, Blom NA. J Rheumatol. 2011;38(12):2682-5.
	Three fetuses with SB and severe myocardial involvement (congenital complete heart block and/or endocardial fibroelastosis) succumbed in utero in spite of treatment.
17882476	FEMALE	Infant
	A case of an infant with flail tricuspid valve due to spontaneous papillary muscle rupture: was neonatal lupus the culprit?
	Fleming GA, Scholl FG, Kavanaugh-McHugh A, Liske MR. Pediatr Cardiol. 2008;29(2):442-5.
	Her underlying diagnosis of autoimmune-mediated heart block with endocardial fibroelastosis and prenatal glucocorticoid steroid treatment represents potentiating factors.
15846168	MIXED_SAMPLE	Infant, Newborn
	Fetal Doppler echocardiographic diagnosis and successful steroid therapy of Luciani-Wenckebach phenomenon and endocardial fibroelastosis related to maternal anti-Ro and anti-La antibodies.
	Raboisson MJ, Fouron JC, Sonesson SE, Nyman M, Proulx F, Gamache S. J Am Soc Echocardiogr. 2005;18(4):375-80.
	Complete fetal heart block (HB) and endocardial fibroelastosis (EFE) are known to be associated with maternal anti-Ro and anti-La antibodies.