Dermatomyositis

A type of idiopathic inflammatory myopathy characterized by evocative skin lesions and symmetrical proximal muscle weakness.

Respiratory distress

Difficulty in breathing. The physical presentation of respiratory distress is generally referred to as labored breathing, while the sensation of respiratory distress is called shortness of breath or dyspnea.


Total: 3

                      


(per page)
PMID (PMCID)
11491505
FEMALE Middle Aged
Hypercapnic coma due to diaphragmatic involvement in a patient with dermatomyositis.
Astudillo LM, Carreiro M, Sailler L, Dingremont CF, Arlet PM.
Clin Exp Rheumatol. 2001;19(4):456-8.
Only few cases of acute respiratory distress in dermatomyositis due to respiratory muscle involvement are reported in literature.
11491505
FEMALE Middle Aged
Hypercapnic coma due to diaphragmatic involvement in a patient with dermatomyositis.
Astudillo LM, Carreiro M, Sailler L, Dingremont CF, Arlet PM.
Clin Exp Rheumatol. 2001;19(4):456-8.
We report an acute respiratory distress by diaphragmatic involvement due to dermatomyositis.
10025861
FEMALE Adult
Dermatomyositis associated with bronchiolitis obliterans organizing pneumonia (BOOP).
Knoell KA, Hook M, Grice DP, Hendrix JD Jr.
J Am Acad Dermatol. 1999;40(2 Pt 2):328-30.
We believe this case shows it is important to recognize that facial rash in the presence of respiratory distress may represent dermatomyositis with BOOP and aggressive treatment may be necessary for resolution of pulmonary symptoms.