Sickle cell anemia

Sickle cell anemias are chronic hemolytic diseases that may induce three types of acute accidents: severe anemia, severe bacterial infections, and ischemic vasoocclusive accidents (VOA) caused by sickle-shaped red blood cells obstructing small blood vessels and capillaries. Many diverse complications can occur.

Proptosis

An eye that is protruding anterior to the plane of the face to a greater extent than is typical.


Total: 5

                       


(per page)
PMID (PMCID)
28938324
 MALE
Bilateral Subperiosteal Hematoma and Orbital Compression Syndrome in Sickle Cell Disease.
Sundu C, Dinc E, Sari A, Unal S, Dursun O.
J Craniofac Surg. 2017;28(8):e775-e776.
A 14-year-old boy with sickle cell disease presented with preseptal cellulitis findings as proptosis, eyelid edema, and hyperemia.
18520831
 MIXED_SAMPLE Child
Orbital compression syndrome in sickle cell disease.
Sokol JA, Baron E, Lantos G, Kazim M.
Ophthalmic Plast Reconstr Surg. 2008;24(3):181-4.
This diagnosis should be considered when a patient with sickle cell disease presents with headache, proptosis, decreased motility, and/or optic nerve compromise.
18520831
 MIXED_SAMPLE Child
Orbital compression syndrome in sickle cell disease.
Sokol JA, Baron E, Lantos G, Kazim M.
Ophthalmic Plast Reconstr Surg. 2008;24(3):181-4.
Three patients with sickle cell disease (2 males aged 22 and 16 years, and a 10-year-old girl) who presented with proptosis, limited ocular motility, and chemosis were found to have an infarction of the marrow space of the greater wing of the sphenoid that produced an orbital subperiosteal hemorrhage and exudate demonstrated on MRI.
3652599
 MALE
Proptosis, skull infarction, and retro-orbital and epidural hematomas in a child with sickle cell disease.
Mallouh AA, Young M, Hamdan J, Salamah MM.
Clin Pediatr (Phila). 1987;26(10):536-8.
A Saudi child with homozygous sickle cell disease (SS) presented with bilateral periorbital swelling, right-sided proptosis, skull bone infarcts, and retro-orbital and epidural hematomas.
3652599
 MALE
Proptosis, skull infarction, and retro-orbital and epidural hematomas in a child with sickle cell disease.
Mallouh AA, Young M, Hamdan J, Salamah MM.
Clin Pediatr (Phila). 1987;26(10):536-8.
Proptosis, skull infarction, and retro-orbital and epidural hematomas in a child with sickle cell disease.