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Sickle cell anemia

Sickle cell anemias are chronic hemolytic diseases that may induce three types of acute accidents: severe anemia, severe bacterial infections, and ischemic vasoocclusive accidents (VOA) caused by sickle-shaped red blood cells obstructing small blood vessels and capillaries. Many diverse complications can occur.

Jaundice

Yellow pigmentation of the skin due to bilirubin, which in turn is the result of increased bilirubin concentration in the bloodstream.

Total: 12

(per page)

PMID (PMCID)
29515745 (5837157)	MALE	Young Adult
	[Occult hepatitis B reactivation in a patient with homozygous sickle cell disease: clinical case and literature review].
	Diop M, Cisse-Diallo VMP, Ka D, Lakhe NA, Diallo-Mbaye K, Massaly A, Dieye A, Fall NM, Badiane AS, Thioub D, Fortes-Deguenonvo L, Lo G, Diop CT, Ndour CT, Soumare M, Seydi M. Pan Afr Med J. 2017;28:127.
	We report the case of a 21-year old patient from Senegal, with homozygous sickle cell disease, presenting with cholestatic jaundice.
26613743 (4671447)	MALE	Adult
	Rare but Lethal Hepatopathy-Sickle Cell Intrahepatic Cholestasis and Management Strategies.
	Malik A, Merchant C, Rao M, Fiore RP. Am J Case Rep. 2015;16:840-3.
	We present the case of a 31-year-old man with past medical history of sickle cell disease and cholecystectomy who was admitted with uncomplicated vaso occlusive crisis and during the hospital stay developed fever, upper abdominal pain, and jaundice.
25386449	OTHER
	Haemoglobin s interaction with Beta thalassaemia- a case report from assam, India.
	Pathak MS, Borah MS, Kalita D. J Clin Diagn Res. 2014;8(9):FD15-6.
	The Hb S carriers (Sickle cell trait) leads a normal life but the Sickle cell disease patients show certain clinical manifestation like joint pain, anaemia and jaundice.
18421713	MALE
	Biloma and pneumobilia in sickle cell disease.
	Lebensburger J, Esbenshade A, Blakely M, Hankins J, Wang W. Pediatr Blood Cancer. 2008;51(2):288-90.
	Spontaneous biloma and pneumobilia developed in a patient with sickle cell disease (SCD) who presented with acute abdominal pain, jaundice, and fever.
17171533	MALE	Middle Aged
	Exacerbation of sickle cell disease itself as a cause of abnormal liver chemistry tests.
	Stanca CM, Fiel MI, Schiano TD. Dig Dis Sci. 2007;52(1):176-8.
	We report the case of a patient presenting with jaundice and abnormal liver biochemistries, without typical evidence of the liver diseases associated with sickle cell anemia.
16215723	FEMALE	Child
	Ischaemic cholangiopathy and sickle cell disease.
	Ahmed M, Dick M, Mieli-Vergani G, Harrison P, Karani J, Dhawan A. Eur J Pediatr. 2006;165(2):112-3.
	We report a case of a 6-year-old girl of Afro-Caribbean origin, known to have sickle cell disease (SCD), with recurrent history of jaundice and abdominal pain.
12883614	FEMALE	Adult
	Pigment polyp in the common bile duct.
	Meshikhes AW, Al-Talaq FT, Al-Faraj AA, Al-Moomen SA. Saudi Med J. 2003;24(7):776-7.
	We report here a case of a young female with sickle cell disease and a past history of open cholecystectomy 10 years ago presenting with intermittent upper abdominal pain and jaundice.
10319541	MALE	Adult
	Hepatic sickling crisis mimicking recurrent cholangitis.
	Mehta S, Nagral A, Sucheta VK, Nagral S, Gopal S, Joshi AS, Krishnamurthy S. Indian J Gastroenterol. 1999;18(2):84-6.
	A 22-year-old man with homozygous sickle cell disease presented with recurrent fever, right upper quadrant pain and jaundice.
8633541	FEMALE	Adult
	Autoimmune hepatitis in a patient with sickle cell disease.
	el Younis CM, Min AD, Fiel MI, Klion FM, Thung SN, Faire B, Miller CM, Bodenheimer HC Jr. Am J Gastroenterol. 1996;91(5):1016-8.
	In this report, we describe the case of a 28-yr-old woman with sickle cell anemia who presented with acute hepatic failure manifested by anorexia, malaise, painless jaundice, elevated aminotransferase activities, and severe coagulopathy.
3292165	MALE	Adult
	Choledochal fungal ball. An unusual cause of biliary obstruction.
	Ho F, Snape WJ Jr, Venegas R, Lechago J, Klein S. Dig Dis Sci. 1988;33(8):1030-4.
	A 31-year-old patient with sickle-cell disease who had previous cholecystectomy developed acute onset of jaundice and abdominal pain.
6698374	FEMALE	Adult
	Hepatic biloma complicating sickle cell disease. A case report and a review of the literature.
	Middleton JP, Wolper JC. Gastroenterology. 1984;86(4):743-4.
	We present a case of right upper quadrant pain, fever, and jaundice in a patient with sickle cell disease.
432694	MALE	Infant, Newborn
	Sickle cell anemia in the neonatal period.
	Karayalcin G. South Med J. 1979;72(4):492-3.
	Although sickle cell anemia rarely presents with clinical manifestations in the newborn period, it should be considered a possible cause of unexplained early jaundice in black newborn infants.