Sickle cell anemia

Sickle cell anemias are chronic hemolytic diseases that may induce three types of acute accidents: severe anemia, severe bacterial infections, and ischemic vasoocclusive accidents (VOA) caused by sickle-shaped red blood cells obstructing small blood vessels and capillaries. Many diverse complications can occur.

Retinal atrophy

Well-demarcated area(s) of partial or complete depigmentation in the fundus, reflecting atrophy of the retinal pigment epithelium with associated retinal photoreceptor loss.

Total: 1

(per page)

PMID (PMCID)
28837721	MALE	Child
	Visual Function in Asymptomatic Patients With Homozygous Sickle Cell Disease and Temporal Macular Atrophy.
	Martin GC, Denier C, Zambrowski O, Grevent D, Bruere L, Brousse V, de Montalembert M, Bremond-Gignac D, Robert MP. JAMA Ophthalmol. 2017;135(10):1100-1105.
	Three patients with sickle cell disease exhibiting preserved visual acuity but showing temporal macular retinal atrophy were included.