Sickle cell anemia

Sickle cell anemias are chronic hemolytic diseases that may induce three types of acute accidents: severe anemia, severe bacterial infections, and ischemic vasoocclusive accidents (VOA) caused by sickle-shaped red blood cells obstructing small blood vessels and capillaries. Many diverse complications can occur.

Single ventricle

The presence of only one working lower chamber in the heart, usually with a virtual absence of the ventricular septum and usually present in conjunction with double inlet left or right ventricle.

Total: 6

(per page)

PMID (PMCID)
26917191	FEMALE	Child
	Staged Single Ventricle Palliation and Homozygous Sickle Cell Disease.
	Maddali MM, Junghare MS, Nishant AR, Kandachar PS, Valliattu J. J Card Surg. 2016;31(4):237-41.
	The successful completion of staged single ventricle palliation in a child with a combination of homozygous sickle cell disease and a single ventricle physiology that tolerate prolonged hypoxemia during earlier stages of Fontan pathway is described.
26917191	FEMALE	Child
	Staged Single Ventricle Palliation and Homozygous Sickle Cell Disease.
	Maddali MM, Junghare MS, Nishant AR, Kandachar PS, Valliattu J. J Card Surg. 2016;31(4):237-41.
	The successful completion of staged single ventricle palliation in a child with a combination of homozygous sickle cell disease and a single ventricle physiology that tolerate prolonged hypoxemia during earlier stages of Fontan pathway is described.
26917191	FEMALE	Child
	Staged Single Ventricle Palliation and Homozygous Sickle Cell Disease.
	Maddali MM, Junghare MS, Nishant AR, Kandachar PS, Valliattu J. J Card Surg. 2016;31(4):237-41.
	Staged Single Ventricle Palliation and Homozygous Sickle Cell Disease.
18172525	FEMALE	Infant, Newborn
	Staged single-ventricle palliation in an infant with hemoglobin SC disease.
	Law MA, Dreyer Z, Heinle JS, Dickerson HA. Tex Heart Inst J. 2007;34(4):439-41.
	Hemoglobin sickle cell disease is associated with anemia and significant vascular sickling sequelae, which increase the risk associated with single-ventricle palliation.
18172525	FEMALE	Infant, Newborn
	Staged single-ventricle palliation in an infant with hemoglobin SC disease.
	Law MA, Dreyer Z, Heinle JS, Dickerson HA. Tex Heart Inst J. 2007;34(4):439-41.
	To our knowledge, there are no reports in the English-language medical literature of single-ventricle palliation having been performed on a patient who had either sickle cell anemia or sickle cell-hemoglobin C disease.
18172525	FEMALE	Infant, Newborn
	Staged single-ventricle palliation in an infant with hemoglobin SC disease.
	Law MA, Dreyer Z, Heinle JS, Dickerson HA. Tex Heart Inst J. 2007;34(4):439-41.
	Herein, we discuss our clinical and surgical management of an infant with tricuspid atresia type IA and hemoglobin sickle cell disease who survived single-ventricle palliative procedures through the 2nd stage of a bidirectional Glenn anastomosis.