Sickle cell anemia

Sickle cell anemias are chronic hemolytic diseases that may induce three types of acute accidents: severe anemia, severe bacterial infections, and ischemic vasoocclusive accidents (VOA) caused by sickle-shaped red blood cells obstructing small blood vessels and capillaries. Many diverse complications can occur.

Respiratory failure

A severe form of respiratory insufficiency characterized by inadequate gas exchange such that the levels of oxygen or carbon dioxide cannot be maintained within normal limits.


Total: 6

                      


(per page)
PMID (PMCID)
29633667
FEMALE Adult
Successful Use of Veno-Venous Extracorporeal Membrane Oxygenation in an Adult Patient with Sickle Cell Anemia and Severe Acute Chest Syndrome.
Sewaralthahab SS, Menaker J, Law JY.
Hemoglobin. 2018;42(1):65-67.
A 25-year-old female with sickle cell anemia presented with respiratory failure due to acute chest syndrome (ACS).
25458459
FEMALE Child
[Acute respiratory distress syndrome complicating an acute chest syndrome: potential benefit of early combination of exchange transfusion and prone positioning].
Dusacre JA, Pons B, Piednoir P, Soubirou JF, Thiery G.
Ann Fr Anesth Reanim. 2014;33(12):700-3.
We report the case of an 8-year-old sickle cell anemia child admitted for acute respiratory failure complicating acute chest syndrome.
24261182
FEMALE Adult
Intravenous gammaglobulin as rescue therapy in a patient with sickle cell and septic shock.
Romero-Legro I, Kadaria D, Murillo LC, Freire AX.
Tenn Med. 2013;106(9):29-31.
We present a case involving a patient with sickle cell and hyposplenism, in which refractory septic shock quickly responded after the infusion of intravenous gammaglobulin (IV-GG) given as an adjuvant-rescue therapy A 30-year-old African-American female with history of Sickle Cell disease was admitted for acute chest syndrome, septic shock and respiratory failure.
22096295
(3214567)
OTHER
Anesthetic management of a patient with sickle cell disease for common bile duct exploration.
Ingle SS, Ubale P.
J Anaesthesiol Clin Pharmacol. 2011;27(4):547-9.
Patients with sickle cell disease (SCD) may present to the anesthetist in different clinical settings like perioperative care, management of acute painful crisis and intensive therapy for acute respiratory failure.
12393443
MIXED_SAMPLE Child
Reversible posterior leukoencephalopathy syndrome and silent cerebral infarcts are associated with severe acute chest syndrome in children with sickle cell disease.
Henderson JN, Noetzel MJ, McKinstry RC, White DA, Armstrong M, DeBaun MR.
Blood. 2003;101(2):415-9.
This study examines patients with sickle cell disease who developed severe episodes of ACS, leading to endotracheal intubation, ventilatory support for respiratory failure, and erythrocytapheresis.
8619401
MALE Adult
Sickle cell acute chest syndrome associated with parvovirus B19 infection: case series and review.
Lowenthal EA, Wells A, Emanuel PD, Player R, Prchal JT.
Am J Hematol. 1996;51(3):207-13.
We present three patients with hemoglobin SC variant of sickle cell disease who developed ACS in association with acute parvovirus B19 infection, one of which died of respiratory failure.