Sickle cell anemia

Sickle cell anemias are chronic hemolytic diseases that may induce three types of acute accidents: severe anemia, severe bacterial infections, and ischemic vasoocclusive accidents (VOA) caused by sickle-shaped red blood cells obstructing small blood vessels and capillaries. Many diverse complications can occur.

Hyperbilirubinemia

An increased amount of bilirubin in the blood.


Total: 9

                      


(per page)
PMID (PMCID)
27366449
OTHER
Perioperative Anaesthetic Approach in a Homozygous Sickle Cell Anaemia Patient with Frequent Pain Crises.
Tuzcu K, Karcoglu M, Davarc I, Hakimoglu S, Akkucuk S.
Turk J Anaesthesiol Reanim. 2014;42(6):348-51.
In patients with sickle cell disease, high rates of erythrocyte generation, degradation, and hyperbilirubinemia increase the risk for cholelithiasis.
16895293
MALE Middle Aged
Case of fatal sickle cell intrahepatic cholestasis despite use of exchange transfusion in an African-American patient.
Costa DB, Miksad RA, Buff MS, Wang Y, Dezube BJ.
J Natl Med Assoc. 2006;98(7):1183-7.
Sickle cell intrahepatic cholestasis (SCIC) is a rare complication of sickle cell anemia, characterized by marked hyperbilirubinemia and acute hepatic failure with an often fatal course.
12394969
MALE Adult
Sickle cell disease, extreme hyperbilirubinemia, and pericardial tamponade: case report and review of the literature.
Khurshid I, Anderson L, Downie GH, Pape GS.
Crit Care Med. 2002;30(10):2363-7.
Sickle cell intrahepatic cholestasis, a potentially fatal complication of sickle cell disease, can present with abdominal pain, acute hepatomegaly, coagulopathy, hyperbilirubinemia, and fulminant hepatic failure.
12394969
MALE Adult
Sickle cell disease, extreme hyperbilirubinemia, and pericardial tamponade: case report and review of the literature.
Khurshid I, Anderson L, Downie GH, Pape GS.
Crit Care Med. 2002;30(10):2363-7.
A 37-yr-old African-American male, with known sickle cell disease, who developed fulminant hepatic failure with subsequent extreme hyperbilirubinemia, coagulopathy, and pericardial tamponade.
8948664
MALE Adult
Delayed hemolytic transfusion reaction due to anti-Go(a), an antibody against the low-prevalence Gonzales antigen.
Larson PJ, Lukas MB, Friedman DF, Manno CS.
Am J Hematol. 1996;53(4):248-50.
A 27-year-old African American male with sickle-cell disease, maintained on chronic transfusion, was noted to have dark plasma during an erythrocytapheresis, procedure, and the pretransfusion hemoglobin was noted to be 1 g/dl lower than 4 weeks before (with hyperbilirubinemia and a significantly increased LDH).
3920595
FEMALE Adult
The unreliability of amniotic fluid bilirubin measurements in isoimmunized pregnancies in sickle cell disease patients.
Hadi HA, Fadel HE, Nelson GH, Hill J.
Obstet Gynecol. 1985;65(5):758-60.
Two patients presented with sickle cell anemia and hyperbilirubinemia who also were isoimmunized.
874660
MIXED_SAMPLE Child
Benign course of extreme hyperbilirubinemia in sickle cell anemia: analysis of six cases.
Buchanan GR, Glader BE.
J Pediatr. 1977;91(1):21-4.
Since the approach to the management and outcome of extreme hyperbilirubinemia in patients with sickle cell anemia is not clearly defined, we reviewed our experience with marked hyperbilirubinemia in six children with sickle cell disease.
874660
MIXED_SAMPLE Child
Benign course of extreme hyperbilirubinemia in sickle cell anemia: analysis of six cases.
Buchanan GR, Glader BE.
J Pediatr. 1977;91(1):21-4.
Since the approach to the management and outcome of extreme hyperbilirubinemia in patients with sickle cell anemia is not clearly defined, we reviewed our experience with marked hyperbilirubinemia in six children with sickle cell disease.
874660
MIXED_SAMPLE Child
Benign course of extreme hyperbilirubinemia in sickle cell anemia: analysis of six cases.
Buchanan GR, Glader BE.
J Pediatr. 1977;91(1):21-4.
Benign course of extreme hyperbilirubinemia in sickle cell anemia: analysis of six cases.