Sickle cell anemia

Sickle cell anemias are chronic hemolytic diseases that may induce three types of acute accidents: severe anemia, severe bacterial infections, and ischemic vasoocclusive accidents (VOA) caused by sickle-shaped red blood cells obstructing small blood vessels and capillaries. Many diverse complications can occur.

Macular atrophy

Well-demarcated area(s) of partial or complete depigmentation in the macula, reflecting atrophy of the retinal pigment epithelium with associated retinal photoreceptor loss.

Total: 3

(per page)

PMID (PMCID)
28837721	MALE	Child
	Visual Function in Asymptomatic Patients With Homozygous Sickle Cell Disease and Temporal Macular Atrophy.
	Martin GC, Denier C, Zambrowski O, Grevent D, Bruere L, Brousse V, de Montalembert M, Bremond-Gignac D, Robert MP. JAMA Ophthalmol. 2017;135(10):1100-1105.
	To assess the visual function of patients with sickle cell disease with no visual symptoms despite temporal macular atrophy.
28837721	MALE	Child
	Visual Function in Asymptomatic Patients With Homozygous Sickle Cell Disease and Temporal Macular Atrophy.
	Martin GC, Denier C, Zambrowski O, Grevent D, Bruere L, Brousse V, de Montalembert M, Bremond-Gignac D, Robert MP. JAMA Ophthalmol. 2017;135(10):1100-1105.
	Temporal macular atrophy in sickle cell disease may have direct consequences on visual function, including in children, even when visual acuity is preserved.
28837721	MALE	Child
	Visual Function in Asymptomatic Patients With Homozygous Sickle Cell Disease and Temporal Macular Atrophy.
	Martin GC, Denier C, Zambrowski O, Grevent D, Bruere L, Brousse V, de Montalembert M, Bremond-Gignac D, Robert MP. JAMA Ophthalmol. 2017;135(10):1100-1105.
	Visual Function in Asymptomatic Patients With Homozygous Sickle Cell Disease and Temporal Macular Atrophy.