Kasabach-Merritt syndrome

Kasabach-Merritt syndrome (KMS), also known as hemangioma-thrombocytopenia syndrome, is a rare disorder characterized by profound thrombocytopenia, microangiopathic hemolytic anemia, and subsequent consumptive coagulopathy in association with vascular tumors, particularly kaposiform hemangioendothelioma or tufted angioma.

Jaundice

Yellow pigmentation of the skin due to bilirubin, which in turn is the result of increased bilirubin concentration in the bloodstream.


Total: 3

                       


(per page)
PMID (PMCID)
26943417
(4595412)
 OTHER
Obstructive jaundice caused by a giant liver hemangioma with Kasabach-Merritt syndrome: a case report.
Yano T, Kobayashi T, Kuroda S, Amano H, Tashiro H, Ohdan H.
Surg Case Rep. 2015;1(1):93.
Obstructive jaundice caused by a giant liver hemangioma with Kasabach-Merritt syndrome: a case report.
19408088
 FEMALE Middle Aged
Superextended hepatectomy for resection of multiple giant hemangiomas: report of a case.
Pachera S, Nishio H, Yamada H, Yokoyama Y, Ebata T, Igami T, Nagino M.
Surg Today. 2009;39(5):452-5.
Serious complications such as jaundice, Kasabach-Merritt syndrome, and rupture are rare.
1928553
 FEMALE Infant
Kaposi-like infantile hemangioendothelioma. A distinctive vascular neoplasm of the retroperitoneum.
Tsang WY, Chan JK.
Am J Surg Pathol. 1991;15(10):982-9.
This lesion was complicated by obstructive jaundice, intestinal obstruction, and thrombocytopenia (Kasabach-Merritt syndrome) leading to intracranial hemorrhage.