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Kasabach-Merritt syndrome

Kasabach-Merritt syndrome (KMS), also known as hemangioma-thrombocytopenia syndrome, is a rare disorder characterized by profound thrombocytopenia, microangiopathic hemolytic anemia, and subsequent consumptive coagulopathy in association with vascular tumors, particularly kaposiform hemangioendothelioma or tufted angioma.

Growth delay

A deficiency or slowing down of growth pre- and postnatally.

Total: 1

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PMID (PMCID)
11893644	MALE	Infant, Newborn
	Case report: Kasabach-Merritt syndrome: a review of the therapeutic options and a case report of successful treatment with radiotherapy and interferon alpha.
	Hesselmann S, Micke O, Marquardt T, Baas S, Bramswig JH, Harms E, Willich N. Br J Radiol. 2002;75(890):180-4.
	Radiation therapy combined with interferon alpha treatment is an alternative treatment modality when high dose corticoid steroid therapy has been ineffective in patients with Kasabach-Merritt syndrome, despite the risks of growth delay and secondary malignancy.