Dubin-Johnson syndrome

Dubin-Johnson syndrome (DJS) is a benign, inherited liver disorder characterized clinically by chronic, predominantly conjugated, hyperbilirubinemia and histopathologically by black-brown pigment deposition in parenchymal liver cells.

Cholestasis

Impairment of bile flow due to obstruction in bile ducts.


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PMID (PMCID)
22544030
 MALE Adult
[A case of sustained cholestasis caused by acute A viral hepatitis in Dubin-Johnson syndrome].
Ra SH, Sung SY, Jung HY, Cha JH, Baik SK, Cho MY, Kim MY.
Korean J Gastroenterol. 2012;59(4):313-6.
It is a first report of cholestasis complicated by acute A viral hepatitis in a patient with Dubin-Johnson syndrome.
22544030
 MALE Adult
[A case of sustained cholestasis caused by acute A viral hepatitis in Dubin-Johnson syndrome].
Ra SH, Sung SY, Jung HY, Cha JH, Baik SK, Cho MY, Kim MY.
Korean J Gastroenterol. 2012;59(4):313-6.
We describe a case of prolonged cholestasis for more than 10 months caused by acute A viral hepatitis in a patient with Dubin-Johnson syndrome.
8924312
 MALE Infant, Newborn
Neonatal cholestasis in two siblings: a variant of Dubin-Johnson syndrome?
Kimura A, Yuge K, Kosai KI, Kage M, Fujisawa T, Inoue T, Yamashita Y, Nakashima E, Kato H.
J Paediatr Child Health. 1995;31(6):557-60.
The elevation of urinary coproporphrin isomer I to more than 90% and the presence cholestasis resembled that in the Dubin-Johnson syndrome, but the hypertriglyceridaemia ( > 1.13 mmol/L as triolein) and the hepatosteatosis differed.
8924312
 MALE Infant, Newborn
Neonatal cholestasis in two siblings: a variant of Dubin-Johnson syndrome?
Kimura A, Yuge K, Kosai KI, Kage M, Fujisawa T, Inoue T, Yamashita Y, Nakashima E, Kato H.
J Paediatr Child Health. 1995;31(6):557-60.
Two Japanese brothers with neonatal cholestasis associated with pigment granules in the hepatocytes and hepatosteatosis were evaluated for the possible role of hepatosteatosis in the Dubin-Johnson syndrome.
8924312
 MALE Infant, Newborn
Neonatal cholestasis in two siblings: a variant of Dubin-Johnson syndrome?
Kimura A, Yuge K, Kosai KI, Kage M, Fujisawa T, Inoue T, Yamashita Y, Nakashima E, Kato H.
J Paediatr Child Health. 1995;31(6):557-60.
Neonatal cholestasis in two siblings: a variant of Dubin-Johnson syndrome?
1336797
 FEMALE Adult
Hepatobiliary complications of oral contraceptives.
Lindberg MC.
J Gen Intern Med. 1992;7(2):199-209.
A final group of women who should avoid oral contraceptives is those with familial defects of biliary excretion, including the Dubin-Johnson syndrome, Rotor's syndrome, and benign intrahepatic recurrent cholestasis.
2035335
 MALE Infant, Newborn
Neonatal Dubin-Johnson syndrome with severe cholestasis: effective phenobarbital therapy.
Kimura A, Ushijima K, Kage M, Mahara R, Tohma M, Inokuchi T, Shibao K, Tanaka N, Fujisawa T, Ono E, et al..
Acta Paediatr Scand. 1991;80(3):381-5.
We described Dubin-Johnson syndrome (DJS) with severe cholestasis in a 20-day-old Japanese boy.
2035335
 MALE Infant, Newborn
Neonatal Dubin-Johnson syndrome with severe cholestasis: effective phenobarbital therapy.
Kimura A, Ushijima K, Kage M, Mahara R, Tohma M, Inokuchi T, Shibao K, Tanaka N, Fujisawa T, Ono E, et al..
Acta Paediatr Scand. 1991;80(3):381-5.
Neonatal Dubin-Johnson syndrome with severe cholestasis: effective phenobarbital therapy.
2400232
 MALE Infant, Newborn
Dubin-Johnson syndrome presenting with neonatal cholestasis.
Shieh CC, Chang MH, Chen CL.
Arch Dis Child. 1990;65(8):898-9.
This case confirms that Dubin-Johnson syndrome is a cause of neonatal cholestasis.
2400232
 MALE Infant, Newborn
Dubin-Johnson syndrome presenting with neonatal cholestasis.
Shieh CC, Chang MH, Chen CL.
Arch Dis Child. 1990;65(8):898-9.
Dubin-Johnson syndrome presenting with neonatal cholestasis.
2400232
 MALE Infant, Newborn
Dubin-Johnson syndrome presenting with neonatal cholestasis.
Shieh CC, Chang MH, Chen CL.
Arch Dis Child. 1990;65(8):898-9.
We report a case of Dubin-Johnson syndrome presenting with neonatal cholestasis.