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Choreoacanthocytosis

Chorea-acanthocytosis (ChAc) is a form of neuroacanthocytosis (see this term) and is characterized clinically by a Huntington disease-like phenotype with progressive neurological symptoms including movement disorders, psychiatric manifestations and cognitive disturbances.

Degeneration of the striatum

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PMID (PMCID)
6727056	FEMALE	Adult
	Neuropathological study of chorea-acanthocytosis.
	Iwata M, Fuse S, Sakuta M, Toyokura Y. Jpn J Med. 1984;23(2):118-22.
	The anatomical substratum of the choreatic involuntary movements in chorea-acanthocytosis is thought to be the degeneration of the striatum, especially the caudate nucleus.