Primary pulmonary lymphoma

Primary pulmonary lymphoma (PPL) is a rare lymphoma of the lung, defined as a clonal lymphoid proliferation affecting one or both lungs (parenchyma and/or bronchi) in a patient with no detectable extrapulmonary involvement at diagnosis or during the subsequent 3 months. PPL comprises low grade/indolent B cell PPL forms, the most frequent form represented by the marginal B-cell lymphoma of mucosa associated lymphoid tissue (MALT lymphoma) and other non-MALT low grade lymphomas; and more rarely high-grade B-cell PPL (including diffuse large B cell lymphoma) and lymphomatoid granulomatosis (LYG).

Neoplasm

An organ or organ-system abnormality that consists of uncontrolled autonomous cell-proliferation which can occur in any part of the body as a benign or malignant neoplasm (tumour).

Total: 3

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PMID (PMCID)
29854536 (5960538)	OTHER
	Primary Pulmonary Anaplastic Large Cell Lymphoma: A Rare Malignancy and Rare Cause of the Luftsichel Sign.
	Von Ende E, Kauffman T, Munoz PA, Martinez-Jimenez S. Case Rep Radiol. 2018;2018:8574642.
	Primary pulmonary lymphomas are rare with primary pulmonary non-Hodgkin lymphoma accounting for only 0.3% of primary lung neoplasms.
25577533	MALE
	[Primary pulmonary mucosa-associated lymphoid tissue lymphoma: a case report].
	Kubisa B, Bochenska A, Piotrowska M, Dec P, Lesinska A, Kubisa A, Wojcik J, Pierog J, Grodzki T. Pneumonol Alergol Pol. 2015;83(1):45-9.
	Primary pulmonary lymphoma accounts only 0,5% of all primary lung neoplasms.
16612936	FEMALE	Middle Aged
	Primary pulmonary lymphoma disguised as asthma.
	Sirmali M, Kalac N, Agackiran Y, Kaya S. Acta Chir Belg. 2006;106(1):127-9.
	Primary pulmonary lymphomas (PPL) only constitute 4% of extra-nodal, non-Hodgkin lymphomas (NHL), less than 1% of NHL in general, and between 0.5% and 1% of malignant pulmonary neoplasms.