A rare, mostly benign, primary tumor of the meninges (arachnoid cap cells), usually located in the supratentorial compartment, commonly appearing in the sixth and seventh decade of life, clinically silent in most cases or causing hyperostosis close to the tumor and resulting in focal bulging and localized pain in less than 10% of cases. Additional features may include headache, seizures, gradual personality changes (apathy and dementia), anosmia, impaired vision, exophthalmos, hearing loss, ataxia, dysmetria, hypotonia, nystagmus, and rarely spontaneous bleeding.
[Dystonia and tremor in bilateral lesion of the posterior mesencephalon and the vermis].
Rousseaux M, Cassim F, Benaim C, Lahousse V, Pruvo JP, Steinling M. Rev Neurol (Paris). 1996;152(12):732-7.
After surgery on a meningioma of the upper part of the fourth ventricle, this patient presented with facial dystonia, predominating on orbicularis muscles and peribuccal area, and limb dystonia, with tonic extension of fingers and first toes.
