Meningioma

A rare, mostly benign, primary tumor of the meninges (arachnoid cap cells), usually located in the supratentorial compartment, commonly appearing in the sixth and seventh decade of life, clinically silent in most cases or causing hyperostosis close to the tumor and resulting in focal bulging and localized pain in less than 10% of cases. Additional features may include headache, seizures, gradual personality changes (apathy and dementia), anosmia, impaired vision, exophthalmos, hearing loss, ataxia, dysmetria, hypotonia, nystagmus, and rarely spontaneous bleeding.

Multiple cafe-au-lait spots

The presence of six or more cafe-au-lait spots.


Total: 1

                      


(per page)
PMID (PMCID)
418361
MIXED_SAMPLE Adult
Meningiomas in five members of a family over two generations, in one member simultaneously with acoustic neurinomas.
Delleman JW, De Jong JG, Bleeker GM.
Neurology. 1978;28(6):567-70.
Another member of the family, however, had multiple meningiomas and bilateral acoustic neurinomas, while yet another had multiple cafe-au-lait spots.