Neurofibroma


Pseudoarthrosis

A pathologic entity characterized by a developmental defect in a long bone leading to bending and pathologic fracture, with inability to form a normal bony callus with subsequent fibrous nonunion, leading to the pseudarthrosis (or \"false joint\").


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PMID (PMCID)
17786009
 MALE Child
Giant malignant nerve sheath tumor of lumbosacral plexus with intraspinal extension in a child with neurofibromatosis type 1.
Pratap A, Nepal P, Agrawal A, Singh MP, Pandey SR.
Pediatr Neurosurg. 2007;43(5):410-3.
Pseudoarthrosis in children has a high rate of association with NF1, and in this case diagnosis of NF1 was supported by development of MPNST in a pre-existing plexiform neurofibroma.