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Linear nevus sebaceus syndrome

Linear nevus sebaceous syndrome (LNSS) is characterized by the association of a large sebaceous nevus, usually appearing on the face or on the scalp, with a broad spectrum of abnormalities that may affect every organ system, including the central nervous system (brain neoplasms, hemimegalencephaly and lateral ventricle enlargement).

Hemiatrophy

Undergrowth of the limbs that affects only one side.

Total: 1

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PMID (PMCID)
11358015	FEMALE	Child
	Desmoplastic neuroepithelial tumor of infancy in the nevus sebaceus syndrome: report of a unique constellation and review of the literature.
	Kopniczky Z, Kobor J, Maraz A, Vajtai I. Pathol Res Pract. 2001;197(4):279-84.
	The nevus sebaceus syndrome (NSS) is a neurocutaneous disorder characterized by unilateral hyperplasia of skin appendages and skeletal hemihypertrophy, hemimegalencephaly, or hemiatrophy along with disabling seizures.