Pachydermoperiostosis

Pachydermoperiostosis (PDP) is a form of primary hypertrophic osteoarthropathy (see this term), a rare hereditary disorder, and is characterized by digital clubbing, pachydermia and subperiosteal new bone formation associated with pain, polyarthritis, <i>cutis verticis gyrata</i>, seborrhea and hyperhidrosis. Three forms have been described: a complete form with pachydermia and periostitis, an incomplete form with evidence of bone abnormalities but lacking pachydermia, and a <i>forme frusta</i> with prominent pachydermia and minimal-to-absent skeletal changes.

Blepharitis

Inflammation of the eyelids.


合計: 1

                      


(表示件数)
PMID (PMCID)
3966121
MALE Middle Aged
Acro-osteolysis associated with hypertrophic pulmonary osteoarthropathy and pachydermoperiostosis.
Joseph B, Chacko V.
Radiology. 1985;154(2):343-4.
The other patient, a 55-year-old man, had pachydermoperiostosis as well as synovial hypertrophy, clubbing of the digits, blepharitis, and a cataract.