Rapidly progressive glomerulonephritis


Granulomatosis

A granulomatous inflammation leading to multiple granuloma formation, which is a specific type of inflammation. A granuloma is a focal compact collection of inflammatory cells, mononuclear cells predominating, usually as a result of the persistence of a non-degradable product and of active cell mediated hypersensitivity.


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PMID (PMCID)
23798092
 MALE Adult
Pulmonary renal syndrome in a case of Wegener's granulomatosis.
Kundu S, Misra S, Halder RK, Roychowdhury A.
Indian J Chest Dis Allied Sci. 2013;55(1):49-52.
We report a case of a 42-year-old patient who presented with Wegener's granulomatosis complicated by pulmonary renal syndrome, i.e., diffuse alveolar haemorrhage and rapidly progressive crescentic glomerulonephritis.
21893452
 MALE Middle Aged
[Granulomatous meningitis, crescentic glomerulonephritis and vasculitis].
Luduena A, Dorado E, Sarano J, Semeniuk G.
Medicina (B Aires). 2011;71(4):369-72.
The diagnostic confirmation of Wegener's granulomatosis based on a positive ANCA test and on the evidence of systemic disease (crescentic glomerulonephritis and involvement of the upper respiratory tract, ears, orbits, peripheral nerves and duramater) allowed a prompt initiation of aggressive immunosuppressive treatment with systemic cyclophosphamide and high - dosis corticosteroids.
18793568
 MALE Middle Aged
Association of idiopathic retroperitoneal fibrosis, rapidly progressive glomerulonephritis and antiproteinase 3 antineutrophil cytoplasmic antibodies (anti PR3-ANCA).
Martinez-Odriozola P, Gutierrez-Macias A, Moina Eguren I, Arrieta Lezama J.
Clin Nephrol. 2008;70(3):251-4.
We report a case of idiopathic retroperitoneal fibrosis and rapidly progressive glomerulonephritis with serum antiproteinase 3 antineutrophil cytoplasmic antibodies (anti-PR3-ANCA), without clinical or histological signs of Wegener's granulomatosis, in a 46-year-old man.
17942646
 MALE Adult
Bivalvular Bartonella henselae prosthetic valve endocarditis.
Vikram HR, Bacani AK, DeValeria PA, Cunningham SA, Cockerill FR 3rd.
J Clin Microbiol. 2007;45(12):4081-4.
Concomitant crescentic glomerulonephritis led to an initial mistaken diagnosis of Wegener's granulomatosis.
15834094
 FEMALE Adult
ANCA associated pauci-immune retinal vasculitis.
Gallagher MJ, Ooi KG, Thomas M, Gavin M.
Br J Ophthalmol. 2005;89(5):608-11.
ANCA associated vasculitides represent distinctive clinicopathological categories--for example, Wegener's granulomatosis, Churg-Strauss syndrome, microscopic polyangiitis, and idiopathic necrotising crescentic glomerulonephritis, collectively known as the small vessel pauci-immune vasculitides.
15619039
 MALE Adult
A case of Wegener's granulomatosis with pulmonary bleeding successfully treated with double filtration plasmapheresis (DFPP).
Iwatani H, Uzu T, Kakihara M, Nakayama Y, Kanasaki K, Yamato M, Hirai Y, Umimoto K, Yamauchi A.
Clin Exp Nephrol. 2004;8(4):369-74.
Renal biopsy showed crescentic glomerulonephritis, and he was diagnosed as having Wegener's granulomatosis.
14677053
 FEMALE
Reversible posterior leukoencephalopathy in a patient with Wegener granulomatosis.
Ohta T, Sakano T, Shiotsu M, Furue T, Ohtani H, Kinoshita Y, Mizoue T, Kiya K, Tanaka I.
Pediatr Nephrol. 2004;19(4):442-4.
A diagnosis of Wegener granulomatosis was made according to the symptom triad of a renal biopsy demonstrating crescentic glomerulonephritis, severe sinusitis, and serological findings of raised proteinase 3 anti-neutrophil cytoplasmic antibody level.
12528081
 MALE Adult
Autoimmune disease complicating antiviral therapy for hepatitis C virus infection.
Wilson LE, Widman D, Dikman SH, Gorevic PD.
Semin Arthritis Rheum. 2002;32(3):163-73.
Skin and renal biopsy specimens showed vasculitis and crescentic glomerulonephritis (GN) in the first case, and typical histologic findings of lupus nephritis in the second; clinical and laboratory features were consistent with Wegener's granulomatosis and SLE, respectively.
11258615
 MIXED_SAMPLE Adult
Three cases of C-ANCA-positive vasculitis treated with immunoadsorption: possible benefit in early treatment.
Matic G, Michelsen A, Hofmann D, Winkler R, Tiess M, Schneidewind JM, Muller W, Ramlow W.
Ther Apher. 2001;5(1):68-72.
Three patients with Wegener's granulomatosis and rapidly progressive glomerulonephritis were treated with an intensified regimen of immunoadsorption (IA) (Excorim or Therasorb) in addition to cyclophosphamide (CYC) and methylprednisolone (PRE).
11236247
 MALE Middle Aged
[A case of rapidly progressive glomerulonephritis in the course of Wegener's granulomatosis].
Idasiak-Piechocka I, Oko A, Lochynska K, Wozniak A, Czekalski S.
Pol Arch Med Wewn. 2000;103(3-4):195-200.
[A case of rapidly progressive glomerulonephritis in the course of Wegener's granulomatosis].
10430990
 MIXED_SAMPLE Adult
Familial occurrence of systemic vasculitis and rapidly progressive glomerulonephritis.
Nowack R, Lehmann H, Flores-Suarez LF, Nanhou A, van der Woude FJ.
Am J Kidney Dis. 1999;34(2):364-73.
In one family, microscopic polyangiitis and rapidly progressive glomerulonephritis occurred in HLA-identical siblings; in the second family, 3 second- and fourth-degree related members were affected by Wegener's granulomatosis.
9519938
 MALE
Wegener's granulomatosis in a patient with apparent drug-induced acute interstitial nephritis.
Haqqie SS, Phelps KR, Singh J, Urizar RE.
Am J Med Sci. 1998;315(3):216-9.
A renal biopsy and serologic testing led instead to the diagnosis of Wegener's granulomatosis (WG) with necrotizing crescentic glomerulonephritis.
8736337
 MALE Middle Aged
Dermatological presentation of disease associated with antineutrophil cytoplasmic antibodies: a report of two contrasting cases and a review of the literature.
Irvine AD, Bruce IN, Walsh M, Burrows D, Handley J.
Br J Dermatol. 1996;134(5):924-8.
Antineutrophil cytoplasmic antibody (ANCA)-associated disease (AAD) constitutes a pathological disease spectrum of a necrotizing vasculitis of small- and medium-sized vessels, extravascular granuloma formation, and necrotizing and crescentic glomerulonephritis, and also a clinical disease continuum which ranges from renal-limited disease to a widespread systemic vasculitis, including Wegener's granulomatosis and microscopic polyangiitis.
8198467
 MIXED_SAMPLE Middle Aged
Mononeuritis multiplex and vasculitis. Association with anti-neutrophil cytoplasmic autoantibody.
Kafka SP, Condemi JJ, Marsh DO, Leddy JP.
Arch Neurol. 1994;51(6):565-8.
Anti-neutrophil cytoplasmic autoantibody (ANCA) has been described in association with Wegener's granulomatosis, polyarteritis nodosa, pauci-immune necrotizing crescentic glomerulonephritis, and so-called ANCA-associated vasculitis.
8344694
 MALE Middle Aged
[Silicosis and systemic diseases].
Siebels M, Schulz V, Andrassy K.
Immun Infekt. 1993;21 Suppl 1:53-4.
We present case histories of 5 patients with silicosis who developed systemic lupus erythematosus and microscopic polyarteritis in two cases each, and rapidly progressive glomerulonephritis (limited Wegener's granulomatosis) in one case.
1468158
 MALE Middle Aged
De novo glomerulonephritis in patients during remission from Wegener's granulomatosis.
Andrassy K, Waldherr R, Erb A, Ritz E.
Clin Nephrol. 1992;38(6):295-8.
In a cohort of 20 consecutive patients with Wegener's granulomatosis and biopsy-proven pauci-immune crescentic glomerulonephritis three patients were in remission, but developed again a nephritic sediment without signs of systemic disease or positive ANCA titers.
2254904
 FEMALE
Microscopic Wegener's disease: a particular form of Wegener's granulomatosis.
Boudes P, Andre C, Belghiti D, Sobel A.
J Rheumatol. 1990;17(10):1412-4.
We describe a case of Wegener's granulomatosis in which the disease was manifested with crescentic glomerulonephritis, upper airway ulcerations, and microangiopathic hemolytic anemia with consumptive coagulopathy.
1968738
 FEMALE
Microscopic polyarteritis: a forgotten aetiology of haemoptysis and rapidly progressive glomerulonephritis.
Zashin S, Fattor R, Fortin D.
Ann Rheum Dis. 1990;49(1):53-6.
The differential diagnosis of haemoptysis with rapidly progressive glomerulonephritis is presented with particular emphasis on Wegener's granulomatosis and microscopic polyarteritis.
3377622
 MIXED_SAMPLE Adult
Periglomerular granulomatosis. A limited form of Wegener's granulomatosis with exclusive renal involvement?
Oliet A, Praga M, Vidaur F, Elosegui A, Usera G, Bello I.
Arch Intern Med. 1988;148(6):1377-9.
The renal biopsy specimens showed a massive periglomerular granulomatosis with crescentic glomerulonephritis.
3593130
 MALE Middle Aged
Wegener's granulomatosis: report of a case with rapidly progressive glomerulonephritis and diabetes mellitus.
Kakoi H, Hiraide F, Nishizawa S, Inouye T, Yoshizawa N.
Auris Nasus Larynx. 1986;13(3):177-89.
Wegener's granulomatosis: report of a case with rapidly progressive glomerulonephritis and diabetes mellitus.