Vascular Ehlers-Danlos syndrome

Ehlers-Danlos syndrome type IV, also known as the vascular type of Ehlers-Danlos syndrome (EDS), is an inherited connective tissue disorder defined by characteristic facial features (acrogeria) in most patients, translucent skin with highly visible subcutaneous vessels on the trunk and lower back, easy bruising, and severe arterial, digestive and uterine complications, which are rarely, if at all, observed in the other forms of EDS.

Thin vermilion border

Reduced width of the skin of vermilion border region of upper lip.


Total: 0

                      


(per page)
PMID (PMCID)