Name: PubCaseFinder
License: http://creativecommons.org/licenses/by/2.1/jp/
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POEMS syndrome

POEMS syndrome is a paraneoplastic syndrome characterized by polyradiculoneuropathy (P), organomegaly (O), endocrinopathy (E), clonal plasma cell disorder (M), and skin changes (S). Other features include papilledema, extravascular volume overload, sclerotic bone lesions, thrombocytosis/erythrocytosis, and elevated VEGF levels.

Polyneuropathy

A generalized disorder of peripheral nerves.

Total: 268

(per page)

PMID (PMCID)
31119772	OTHER
	Adenopathy and extensive skin patch overlying a plasmacytoma with unusual histologic findings in a patient with polyneuropathy, organomegaly, endocrinopathy, monoclonal protein and skin changes syndrome and Castleman disease.
	Dagrosa AT, Cowdrey MCE, LeBlanc RE, Lansigan F, Kaur P, Carter JB. J Cutan Pathol. 2019;:.
	The patient subsequently developed polyneuropathy and peripheral edema, which supported an additional diagnosis of polyneuropathy, organomegaly, endocrinopathy, monoclonal protein, and skin changes (POEMS) syndrome.
31119772	OTHER
	Adenopathy and extensive skin patch overlying a plasmacytoma with unusual histologic findings in a patient with polyneuropathy, organomegaly, endocrinopathy, monoclonal protein and skin changes syndrome and Castleman disease.
	Dagrosa AT, Cowdrey MCE, LeBlanc RE, Lansigan F, Kaur P, Carter JB. J Cutan Pathol. 2019;:.
	The patient subsequently developed polyneuropathy and peripheral edema, which supported an additional diagnosis of polyneuropathy, organomegaly, endocrinopathy, monoclonal protein, and skin changes (POEMS) syndrome.
30847222	OTHER
	Effectiveness of pulmonary vasodilators on pulmonary hypertension associated with POEMS syndrome.
	Ohashi K, Nishimura R, Sugimoto S, Sakao S, Tanabe N, Tatsumi K. Respirol Case Rep. 2019;7(4):e00411.
	Polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (POEMS) syndrome is a rare plasma cell disease.
30713387	OTHER
	Positron Emission Tomography-Computed Tomography in a Case of POEMS Syndrome.
	Infante JR, Garcia L, Rayo JI, Serrano J, Moreno M, Cobo A, Jimenez P, Martinez A. Indian J Nucl Med. 2019;34(1):66-68.
	The POEMS syndrome is a rare and multisystemic disease characterized by the presence of polyneuropathy, organomegaly, endocrinopathy, presence of M protein, and alterations in the skin.
30632181	MIXED_SAMPLE	Middle Aged
	Tufted-angioma-like lesion associated with vascular endothelial growth factor and interleukin-6 in TAFRO syndrome: Is it a common histological feature of multicentric Castleman disease/POEMS syndrome?
	Fujita K, Hatta K. J Cutan Pathol. 2019;46(4):280-284.
	The lesions resembled a tufted angioma, although those of case 1 partially resembled a glomeruloid hemangioma, which was known as a specific lesion in POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, M-protein and skin changes), a variant of multicentric Castleman disease (MCD).
29893339	MALE	Middle Aged
	An atypical presentation of POEMS syndrome with IgG kappa type M protein and normal VEGF level: Case report and review of literature.
	Pulivarthi S, Gurram MK. J Cancer Res Ther. 2018;14(3):679-681.
	We present an atypical case of POEMS syndrome with subclinical polyneuropathy, splenomegaly, hypogonadism, and myeloma of immunoglobulin G kappa type.
29893339	MALE	Middle Aged
	An atypical presentation of POEMS syndrome with IgG kappa type M protein and normal VEGF level: Case report and review of literature.
	Pulivarthi S, Gurram MK. J Cancer Res Ther. 2018;14(3):679-681.
	POEMS syndrome is a multisystem disorder characterized by polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes.
29739345 (5938810)	MALE	Middle Aged
	Atypical central retinal artery occlusion as the first presentation of POEMS syndrome: a case report.
	Jindahra P, Dejthevaporn C, Niparuck P, Waisayarat J, Cheecharoen P, Threetong T, Petpiroon P, Sujirakul T, Poonyathalang A, Vanikieti K. BMC Neurol. 2018;18(1):64.
	After extensive investigations, diagnosis of "POEMS syndrome" was made based on polyneuropathy, elevated lambda light chain level, elevated plasma vascular endothelial growth factor (VEGF), hepatomegaly, spinal sclerotic bone lesions, and thrombocytosis.
29739345 (5938810)	MALE	Middle Aged
	Atypical central retinal artery occlusion as the first presentation of POEMS syndrome: a case report.
	Jindahra P, Dejthevaporn C, Niparuck P, Waisayarat J, Cheecharoen P, Threetong T, Petpiroon P, Sujirakul T, Poonyathalang A, Vanikieti K. BMC Neurol. 2018;18(1):64.
	POEMS syndrome is a plasma cell disorder, which clinically manifests from paraneoplastic syndrome: polyneuropathy, organomegaly, endocrinopathy, monoclonal plasma cell disorder, and skin changes.
30301456 (6176504)	MALE
	Castleman disease of the hyaline vascular variant transforming to POEMS syndrome as endpoint: a case report.
	Ge Y, Da Q, Dai Y. BMC Neurol. 2018;18(1):169.
	Here we report a 66-year-old man with treated Castleman disease developing with sequential presence of endocrinopathy polyneuropathy, skin changes, organomegaly and extravascular volume overload within 18years, which was finally confirmed as POEMS syndrome by positive monoclonal protein.
30301456 (6176504)	MALE
	Castleman disease of the hyaline vascular variant transforming to POEMS syndrome as endpoint: a case report.
	Ge Y, Da Q, Dai Y. BMC Neurol. 2018;18(1):169.
	We report a rare case that triggers the need to consider POEMS syndrome diagnosis for patients carrying Castleman disease and polyneuropathy.
29861185	FEMALE
	Cutaneous Mycobacterium chelonae infection following autologous peripheral blood stem cell transplantation for POEMS syndrome.
	Hashimoto Y, Ikeda A, Tokuyasu Y, Omura H, Tanaka T. J Infect Chemother. 2018;24(12):983-986.
	We experienced a case who received an autologous peripheral blood stem cell transplantation (Auto-PBSCT) for POEMS syndrome (polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes) and developed cutaneous Mycobacterium chelonae infection.
30665482	FEMALE	Middle Aged
	Glomeruloid Hemangioma as a Late Manifestation of POEMS Syndrome.
	Moreira Amorim G, Sodre C, Mastrangelo Marinho Falcao E, Fernandes Timbo R, Cuzzi T, Ramos-E-Silva M. Acta Dermatovenerol Croat. 2018;26(4):321-324.
	Glomeruloid hemangiomas were first described by Chan in 1990 as a cutaneous marker of POEMS syndrome (Polyneuropathy, Organomegaly, Endocrinopathy, Monoclonal proteinemia, and Skin changes).
30273192	FEMALE	Middle Aged
	Increased Risk of Ischemic Stroke in Multiple Myeloma Associated With Lenalidomide Treatment: A Case Report and Review of the Literature.
	de Celis E, Alonso de Lecinana M, Rodriguez-Pardo J, Fuentes B, Diez-Tejedor E. Clin Neuropharmacol. 2018;41(6):232-235.
	A literature review provided 84 reports from the license holder, 2 more cases of stroke in patients with MM receiving lenalidomide and a recurrent stroke in a patient experiencing polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (POEMS syndrome) treated with lenalidomide.
29467805	OTHER
	Reduction of Optic Disc Oedema by Bortezomib and Dexamethasone Followed by Autologous Peripheral Blood Stem Cell Transplantation in Patient with POEMS Syndrome.
	Iwase T, Yokouchi H, Misawa S, Oshitari T, Baba T, Kuwabara S, Yamamoto S. Neuroophthalmology. 2018;42(1):25-30.
	The authors present findings in a 39-year-old man with polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (POEMS) syndrome with bilateral optic disc oedema.
29100675	MALE	Middle Aged
	Skull base plasmacytoma: A unique case of POEMS syndrome with a plasmacytoma causing craniocervical instability.
	Gilder H, Murphy ME, Alvi MA, Kerezoudis P, Shepherd D, Maloney PR, Yaszemski MJ, Morris JM, Dispenzieri A, Matsumoto JM, Bydon M. J Clin Neurosci. 2018;47:254-257.
	Plasmacytomas often present as a collection of findings known as POEMS-syndrome (Polyneuropathy, Organomegaly, Endocrinopathy, M-Protein spike, and Skin changes).
30587749	FEMALE
	[Video-assisted Thoracoscopic Pericardial Fenestration for Pericardial Effusion in a Patient with Crow-Fukase Syndrome].
	Nishimoto T, Bonkohara Y, Murakami H, Noma D. Kyobu Geka. 2018;71(13):1092-1095.
	Therefore, she was diagnosed with Crow-Fukase (polyneuropathy, organomegaly, endocrinopathy, M protein, skin changes: POEMS) syndrome, which is characterized by the presence of plasma cell dyscrasia with them.
29056130	FEMALE	Adult
	An Adult with Polyneuropathy and Hypogonadism due to Poems Syndrome.
	Zaidi S, Sattar S, Asumal KB. J Coll Physicians Surg Pak. 2017;27(10):651-653.
	An Adult with Polyneuropathy and Hypogonadism due to Poems Syndrome.
28405536 (5384847)	OTHER
	An Unfortunate Polyneuropathy, Organomegaly, Endocrinopathy, Monoclonal Gammopathy, and Skin Change (POEMS).
	Afridi F, Otoya J, Bunting SF, Chaaya G. Cureus. 2017;9(3):e1086.
	POEMS syndrome is an acronym for polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy and skin changes, which is a rare paraneoplastic disease of monoclonal plasma cells.
28664017 (5364899)	OTHER
	Coexistence of Quasi-moyamoya Disease and POEMS Syndrome in a Patient with Intracranial Hemorrhage: A Case Report and Literature Review.
	Yamaguchi I, Satomi J, Yamamoto N, Yoshioka S, Tada Y, Yagi K, Kanematsu Y, Nagahiro S. NMC Case Rep J. 2017;4(1):5-9.
	We suggest that the POEMS syndrome be ruled out in the differential diagnosis of patients presenting with atypical stroke, multivessel stenotic lesions (moyamoya vessels), and polyneuropathy.